Ahmed Said Abdirahman, Karataş Mesut, Öcal Lütfi, Hassan Mohamed Sheikh, Mohamud Mohmed Abdullahi, Hassan Mohamed Omar, Dirie Abdirahman Mohamed Hassan, Waberi Mohamud Mire, Ali Abdijalil Abdullahi
Cardiology Department at Mogadishu Somali-Turkish Training and Research Hospital, Mogadishu, Somalia.
Neurology Department at Mogadishu Somali-Turkish Training and Research Hospital, Mogadishu, Somalia.
Ann Med Surg (Lond). 2022 Sep 1;81:104543. doi: 10.1016/j.amsu.2022.104543. eCollection 2022 Sep.
and importance: Isolated left ventricular noncompaction cardiomyopathy (LVNC), uncommon type of primary hereditary cardiomyopathy. It is a spongy morphological appearance of the myocardium that occurs largely in the LV.
We discuss here a case of 19 years old female with no known past medical history who present with Shortness of breath (SOB) and left sided weakness following delivery.Bedside Echocardiography demonstrated Left ventricular trabiculation with reduced ejection fraction. While brain Computed tomography showed acute ischemic stroke primly due to non-compaction cardiomyopathy as the embolic. Patient was discharged after successfully managed.
Left ventricular non-compaction cardiomyopathy (LVNC) is characterized by progressive ventricular trabeculation and deep intratrabecular recesses caused by the functional arrest of myocardial maturation, which is a rare case of congenital cardiomyopathy. Our patient had isolated non-compaction cardiomyopathy of the type that was complicated by an acute ischemic stroke and was treated accordingly.
It is usually associated with congenital heart disease, but isolated left ventricular non-compaction cardiomyopathy is very uncommon.
及其重要性：孤立性左心室心肌致密化不全心肌病（LVNC），是一种罕见的原发性遗传性心肌病。它是心肌的一种海绵状形态表现，主要发生在左心室。
我们在此讨论一名19岁女性病例，既往无已知病史，产后出现呼吸急促（SOB）和左侧肢体无力。床旁超声心动图显示左心室肌小梁增多，射血分数降低。而脑部计算机断层扫描显示急性缺血性中风主要是由于致密化不全心肌病作为栓子所致。患者经成功治疗后出院。
左心室心肌致密化不全心肌病（LVNC）的特征是心肌成熟功能停滞导致进行性心室肌小梁增多和肌小梁内深陷，这是一种罕见的先天性心肌病病例。我们的患者患有孤立性致密化不全心肌病，并发急性缺血性中风，并据此进行了治疗。
它通常与先天性心脏病有关，但孤立性左心室心肌致密化不全心肌病非常罕见。
