镰状细胞病的胃肠道血管阻塞性危机
Gastrointestinal vaso-occlusive crisis in sickle cell disease.
作者信息
Gautam Garima, Harmon Robert, Foley Raymond
机构信息
Department of Internal Medicine, University of Connecticut, UConn Health, Farmington, Connecticut.
出版信息
Proc (Bayl Univ Med Cent). 2022 Aug 15;35(6):856-857. doi: 10.1080/08998280.2022.2108995. eCollection 2022.
Abstract
Although rare, gastrointestinal vaso-occlusive crisis in sickle cell disease results in potentially life-threatening ischemia and death. Here we present a case of a 34-year-old patient with sickle cell disease who developed an acute pain crisis complicated by hypovolemia, hypoxia, and hypotension. The patient was treated with supportive measures. Diagnosis can be challenging and difficult to differentiate from usual pain crisis.
摘要
尽管罕见，但镰状细胞病中的胃肠道血管闭塞危机会导致潜在的危及生命的缺血和死亡。在此，我们报告一例34岁的镰状细胞病患者，该患者发生了急性疼痛危机，并伴有低血容量、缺氧和低血压。患者接受了支持性治疗。诊断可能具有挑战性，且难以与常见的疼痛危机相区分。
相似文献
1
Gastrointestinal vaso-occlusive crisis in sickle cell disease.镰状细胞病的胃肠道血管阻塞性危机
Proc (Bayl Univ Med Cent). 2022 Aug 15;35(6):856-857. doi: 10.1080/08998280.2022.2108995. eCollection 2022.
2
Addressing challenges of clinical trials in acute pain: The Pain Management of Vaso-occlusive Crisis in Children and Young Adults with Sickle Cell Disease Study.应对急性疼痛临床试验的挑战：镰状细胞病儿童和青年血管闭塞性危机的疼痛管理研究。
Clin Trials. 2016 Aug;13(4):409-16. doi: 10.1177/1740774516636573. Epub 2016 Mar 21.
3
Acute gastrointestinal vaso-occlusive ischemia in sickle cell disease: CT imaging features and clinical outcome.镰状细胞病中的急性胃肠道血管阻塞性缺血：CT 成像特征和临床转归。
Abdom Radiol (NY). 2016 Mar;41(3):466-75. doi: 10.1007/s00261-015-0621-7.
4
Sevuparin for the treatment of acute pain crisis in patients with sickle cell disease: a multicentre, randomised, double-blind, placebo-controlled, phase 2 trial.沙利度胺治疗镰状细胞病患者急性疼痛危象的多中心、随机、双盲、安慰剂对照 2 期临床试验。
Lancet Haematol. 2021 May;8(5):e334-e343. doi: 10.1016/S2352-3026(21)00053-3.
5
Subclinical myocardial injury during vaso-occlusive crisis in pediatric sickle cell disease.小儿镰状细胞病血管阻塞危象期间的亚临床心肌损伤。
Eur J Pediatr. 2018 Dec;177(12):1745-1752. doi: 10.1007/s00431-018-3231-x. Epub 2018 Sep 7.
6
Exacerbation of oxidative stress during sickle vaso-occlusive crisis is associated with decreased anti-band 3 autoantibodies rate and increased red blood cell-derived microparticle level: a prospective study.镰状细胞血管闭塞危象期间氧化应激的加剧与抗带3自身抗体率降低和红细胞衍生微粒水平升高相关：一项前瞻性研究。
Br J Haematol. 2017 Mar;176(5):805-813. doi: 10.1111/bjh.14476. Epub 2016 Dec 16.
7
Diagnosis of Bone Marrow Necrosis following Severe Vaso-Occlusive Crisis in Patient with Compound Heterozygous Sickle Cell Disease.复合杂合子型镰状细胞病患者严重血管闭塞危象后骨髓坏死的诊断
Transfus Med Hemother. 2023 Mar 7;50(4):360-364. doi: 10.1159/000529500. eCollection 2023 Aug.
8
Magnetic Resonance Imaging Assessment of Kidney Oxygenation and Perfusion During Sickle Cell Vaso-occlusive Crises.磁共振成像评估镰状细胞血管阻塞危象期间肾脏的氧合和灌注。
Am J Kidney Dis. 2017 Jan;69(1):51-59. doi: 10.1053/j.ajkd.2016.07.027. Epub 2016 Sep 20.
9
Vaso-Occlusive Pain Management in a Patient With Sickle Cell Disease Associated With Moyamoya Syndrome.镰状细胞病合并烟雾病综合征患者的血管闭塞性疼痛管理
Cureus. 2022 Mar 30;14(3):e23667. doi: 10.7759/cureus.23667. eCollection 2022 Mar.
10
Effect of ketorolac in pediatric sickle cell vaso-occlusive pain crisis.酮咯酸在小儿镰状细胞血管阻塞性疼痛危象中的作用
Pediatr Emerg Care. 1999 Jun;15(3):179-82. doi: 10.1097/00006565-199906000-00004.
本文引用的文献
1
The vaso-occlusive pain crisis in sickle cell disease: Definition, pathophysiology, and management.镰状细胞病的血管阻塞性疼痛危象：定义、病理生理学和治疗。
Eur J Haematol. 2020 Sep;105(3):237-246. doi: 10.1111/ejh.13430. Epub 2020 May 19.
2
Ischemic Colitis in Sickle Cell Disease: A Case Report of a Diagnostic Challenge.镰状细胞病中的缺血性结肠炎：一例诊断难题的病例报告
Case Rep Gastrointest Med. 2018 Jan 24;2018:2358091. doi: 10.1155/2018/2358091. eCollection 2018.
3
CT of Gastrointestinal Vasoocclusive Crisis Complicating Sickle Cell Disease.CT 诊断胃肠道血管阻塞性危象并发镰状细胞病
AJR Am J Roentgenol. 2015 May;204(5):994-9. doi: 10.2214/AJR.14.13286.
4
A unique cause of intestinal and splenic infarction in a sickle cell trait patient.一名镰状细胞性状患者肠道和脾脏梗死的独特病因。
Case Rep Surg. 2013;2013:580453. doi: 10.1155/2013/580453. Epub 2013 May 7.
5
Sickle cell biomechanics.镰状细胞生物力学。
Annu Rev Biomed Eng. 2010 Aug 15;12:345-67. doi: 10.1146/annurev-bioeng-070909-105339.
6
Gastrointestinal and hepatic complications of sickle cell disease.镰状细胞病的胃肠道和肝脏并发症。
Clin Gastroenterol Hepatol. 2010 Jun;8(6):483-9; quiz e70. doi: 10.1016/j.cgh.2010.02.016. Epub 2010 Mar 6.
7
Approach to the vaso-occlusive crisis in adults with sickle cell disease.成人镰状细胞病血管闭塞性危象的处理方法
Am Fam Physician. 2000 Mar 1;61(5):1349-56, 1363-4.
8
Ischemic colitis complicating sickle cell crisis.缺血性结肠炎并发镰状细胞危象。
Gastroenterology. 1983 Jan;84(1):171-4.
Zotero 插件