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附睾肺泡状横纹肌肉瘤:一例报告。

Alveolar rhabdomyosarcoma of epididymis: A case report.

作者信息

Liang Xiangyi, Wang Shun, Li Tao, Liu Longlong, Duan Yu, Luo Yuting, Wang Qing, Hu Jianxin, Jiang Kehua

机构信息

Guizhou Provincial People's Hospital, Guizhou, China.

出版信息

Front Oncol. 2022 Nov 2;12:1027504. doi: 10.3389/fonc.2022.1027504. eCollection 2022.

DOI:10.3389/fonc.2022.1027504
PMID:36408167
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9666769/
Abstract

Rhabdomyosarcoma (RMS) is a soft tissue tumor, which is the most common in the head, neck, limbs, and trunk. RMS originating from the epididymis is extremely rare. Herein, we reported a 34-year-old patient with RMS on the right epididymis. For this case, right epididymal mass resection was performed and intraoperative freezing suggested a malignant tumor. Right testicular radical resection was subsequently adopted, with right epididymal alveolar RMS being pathologically diagnosed. Alternating VAC/VI chemotherapy was given after surgery, and tumor recurrence has not been found so far.

摘要

横纹肌肉瘤(RMS)是一种软组织肿瘤,在头、颈、四肢和躯干中最为常见。起源于附睾的RMS极为罕见。在此,我们报告了一名34岁的右侧附睾RMS患者。针对该病例,进行了右侧附睾肿物切除术,术中冰冻提示为恶性肿瘤。随后采取了右侧睾丸根治性切除术,病理诊断为右侧附睾腺泡状RMS。术后给予VAC/VI交替化疗,目前尚未发现肿瘤复发。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/492f/9666769/50b190f4860f/fonc-12-1027504-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/492f/9666769/41e59927b352/fonc-12-1027504-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/492f/9666769/50b190f4860f/fonc-12-1027504-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/492f/9666769/41e59927b352/fonc-12-1027504-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/492f/9666769/50b190f4860f/fonc-12-1027504-g002.jpg

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Int Cancer Conf J. 2019 Jun 15;8(4):175-180. doi: 10.1007/s13691-019-00378-2. eCollection 2019 Oct.
2
Demographic and Treatment Variables Influencing Outcome for Localized Paratesticular Rhabdomyosarcoma: Results From a Pooled Analysis of North American and European Cooperative Groups.影响局限性睾丸旁横纹肌肉瘤预后的人口统计学和治疗变量:北美和欧洲合作组的汇总分析结果
J Clin Oncol. 2018 Oct 23;36(35):JCO2018789388. doi: 10.1200/JCO.2018.78.9388.
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Addition of Vincristine and Irinotecan to Vincristine, Dactinomycin, and Cyclophosphamide Does Not Improve Outcome for Intermediate-Risk Rhabdomyosarcoma: A Report From the Children's Oncology Group.
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Pan Afr Med J. 2014 Nov 14;19:279. doi: 10.11604/pamj.2014.19.279.4784. eCollection 2014.
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