Shah Rahulkumar, Gupta Rahul, Aiyer Ranjan
Department of ENT and Head- Neck Surgery, Baroda Medical College, Vadodara, Gujarat India.
Indian J Otolaryngol Head Neck Surg. 2022 Oct;74(Suppl 2):1274-1280. doi: 10.1007/s12070-021-02387-1. Epub 2021 Jan 26.
Hemangiopericytomas (HPCs) are rare vascular tumours originating from extra capillary cells called Zimmermann's pericytes. Only 5% of these lesions occur in the Sino nasal cavity. Sino nasal HPCs have a benign course with a high recurrence rate ranging from 9.5 to 50%. A radical surgical resection is considered the gold standard treatment either via external approach (lateral rhinotomy or Caldwell-Luc) or endoscopic approach. Three cases of Sino nasal hemangiopericytomas were treated at our institute. All these cases were operated via endoscopic approach. We are reporting their diagnostic work-up and the therapeutic management as case series. We also discuss epidemiological, clinical, morpho-pathological and radiological characteristics of this tumoral pathology. A treatment plan is also elucidated which may help to develop a long term treatment protocol for these lesions.
血管外皮细胞瘤(HPCs)是一种罕见的血管肿瘤,起源于称为齐默尔曼周细胞的毛细血管外细胞。这些病变中只有5%发生在鼻腔鼻窦。鼻腔鼻窦HPCs病程良性,但复发率较高,为9.5%至50%。根治性手术切除被认为是金标准治疗方法,可通过外部入路(侧鼻切开术或柯-陆氏手术)或内镜入路进行。我院治疗了3例鼻腔鼻窦血管外皮细胞瘤。所有这些病例均通过内镜入路进行手术。我们将其诊断检查和治疗管理作为病例系列进行报告。我们还讨论了这种肿瘤病理学的流行病学、临床、形态病理学和放射学特征。此外,还阐明了一个治疗方案,这可能有助于制定针对这些病变的长期治疗方案。