Bashizadehfakhar Hoorieh, Panjnoush Mehrdad, Kheirandish Yasaman, Sedaghati Azin, Mirjalili Faezeh, Aliasghari Abandansari Sara
Dental Research Center, Dentistry Research Institute, Tehran University of Medical Sciences, Tehran, Iran.
Department of Dentomaxillofacial Radiology, School of Dentistry, Tehran University of Medical Sciences, Tehran, Iran.
Front Dent. 2022 Aug 11;19:27. doi: 10.18502/fid.v19i27.10598. eCollection 2022.
Congenital diffuse infiltrating lipomatosis of the face (CDIL-F) is a rare clinicopathological entity with an unknown etiology, in which mature adipose tissue infiltrates the soft tissue structures in one side, and causes considerable asymmetry. Herein, we report a case of CDIL-F who underwent many surgical procedures without definite diagnosis during 12 years. CDIL-F presents symptoms with various severity levels due to infiltration of adipose tissue that makes removal difficult. Thus, it is recommended to inform patients about the high rate of recurrence.
先天性面部弥漫性浸润性脂肪瘤病(CDIL-F)是一种病因不明的罕见临床病理实体,其中成熟脂肪组织浸润一侧的软组织结构,导致明显的不对称。在此,我们报告一例CDIL-F患者,其在12年中接受了多次手术,但未得到明确诊断。由于脂肪组织浸润,CDIL-F的症状严重程度各异,这使得切除困难。因此,建议告知患者复发率较高。