The Center for RNA Biomedicine and the Department of Human Genetics, University of Michigan, Ann Arbor, MI 48109, U.S.A.
Biochem Soc Trans. 2022 Dec 16;50(6):1715-1724. doi: 10.1042/BST20220549.
Maintenance of proteostasis is of utmost importance to cellular viability and relies on the coordination of many post-transcriptional processes to respond to stressful stimuli. Stress granules (SGs) are RNA-protein condensates that form after translation initiation is inhibited, such as during the integrated stress response (ISR), and may facilitate cellular adaptation to stress. The ribosome-associated quality control (RQC) pathway is a critical translation monitoring system that recognizes aberrant mRNAs encoding potentially toxic nascent peptides to target them for degradation. Both SG regulation and the RQC pathway are directly associated with translation regulation, thus it is of no surprise recent developments have demonstrated a connection between them. VCP's function in the stress activated RQC pathway, ribosome collisions activating the ISR, and the regulation of the 40S ribosomal subunit by canonical SG proteins during the RQC all connect SGs to the RQC pathway. Because mutations in genes that are involved in both SG and RQC regulation are associated with degenerative and neurological diseases, understanding the coordination and interregulation of SGs and RQC may shed light on disease mechanisms. This minireview will highlight recent advances in understanding how SGs and the RQC pathway interact in health and disease contexts.
维持蛋白质稳态对细胞活力至关重要,依赖于许多转录后过程的协调,以响应应激刺激。应激颗粒(SGs)是在翻译起始被抑制后形成的 RNA-蛋白质凝聚物,例如在整合应激反应(ISR)期间,并且可能促进细胞适应应激。核糖体相关质量控制(RQC)途径是一种关键的翻译监测系统,它识别编码潜在毒性新生肽的异常 mRNA,将其靶向降解。SG 调节和 RQC 途径都与翻译调节直接相关,因此最近的发展表明它们之间存在联系也就不足为奇了。VCP 在应激激活的 RQC 途径中的功能、核糖体碰撞激活 ISR 以及在 RQC 期间规范 SG 蛋白对 40S 核糖体亚基的调节,都将 SGs 与 RQC 途径联系起来。由于参与 SG 和 RQC 调节的基因突变与退行性和神经疾病有关,因此了解 SGs 和 RQC 的协调和相互调节可能有助于阐明疾病机制。这篇综述将重点介绍在健康和疾病背景下理解 SGs 和 RQC 途径相互作用的最新进展。