Sassi Farah, Sahraoui Ghada, Charfi Lamia, Ines Zemni, Mrad Karima, Doghri Raoudha
Pathology Department, Salah Azaiez Institute, Tunis, Tunisia.
Research Laboratory LR21SP01, Salah Azaiez Institute Tunis, Tunisia.
Rare Tumors. 2022 Dec 23;14:20363613221148839. doi: 10.1177/20363613221148839. eCollection 2022.
Myxoid liposarcoma (MLPS) is the second most prevalent subtype of liposarcoma. It is usually found in the deep tissues of the lower limbs and rarely in gynecologic tract. Herein we present the second case in the English literature of a primary MLPS arising from the broad ligament which was thought to be a borderline ovarian tumor. The aim is to discuss its clinical and pathological characteristics. A 42-year-old woman presented with pelvic pain for the last 6 months. Magnetic resonance imaging was not specific. She underwent a surgical resection of the tumor mass, and pathological examination confirmed the diagnosis of MLPS deriving from the broad ligament. She received radiotherapy and the patient is doing well at 3 months follow-up. The clinical aspects, pathological diagnosis, prognosis, and therapy approach of broad ligament MLPS are all poorly understood. Complete surgical resection with or without radiotherapy is the mainstay of treatment in located MLPS.
黏液样脂肪肉瘤(MLPS)是脂肪肉瘤中第二常见的亚型。它通常发生于下肢深部组织,很少见于生殖道。在此,我们报告英文文献中第二例起源于阔韧带的原发性MLPS病例,该病例最初被认为是交界性卵巢肿瘤。目的是讨论其临床和病理特征。一名42岁女性在过去6个月出现盆腔疼痛。磁共振成像结果不具有特异性。她接受了肿瘤肿块的手术切除,病理检查确诊为起源于阔韧带的MLPS。她接受了放疗,在3个月的随访中患者情况良好。阔韧带MLPS的临床特征、病理诊断、预后及治疗方法均了解甚少。对于局限性MLPS,完整手术切除联合或不联合放疗是主要治疗方法。