Vershinina K Ia, Grinberg I I
Arkh Patol. 1987;49(6):63-6.
A case of hemochromatosis--a disease in which iron is deposited in parenchymatous organs in the form of hemosiderin leading to fibrosis and functional impairment of these organs--is reported. The classical triad of symptoms seen in hemochromatosis (cirrhosis of the liver, diabetes mellitus, and skin pigmentation) are often supplemented by cardiomyopathy. In this case, postmortem examination revealed pigmentary cirrhosis of the liver and pancreas and hemosiderin deposits in the myocardium and other organs. The leading cause of death was concluded to be hemochromatosis of the heart.
报告了一例血色素沉着症病例，血色素沉着症是一种铁以含铁血黄素的形式沉积在实质器官中，导致这些器官纤维化和功能受损的疾病。血色素沉着症常见的典型三联征症状（肝硬化、糖尿病和皮肤色素沉着）常伴有心肌病。在该病例中，尸检发现肝脏和胰腺呈色素性肝硬化，心肌和其他器官有含铁血黄素沉积。死亡的主要原因被判定为心脏血色素沉着症。
