Panigrahi Chinmayee, Mishra Pritinanda, Pati Akash Bihari, Das Kanishka, Sable Mukund
Department of Pathology and Lab Medicine, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India.
Department of Paediatric Surgery, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India.
Indian J Pathol Microbiol. 2023 Jan-Mar;66(1):145-147. doi: 10.4103/ijpm.ijpm_677_21.
Ovarian Sertoli Leydig cell tumors (SLCT) accounts for less than 0.5% of all ovarian malignancies. The incidence of primary extra-ovarian SLCT is extremely rare with reported cases occurring in young adult women till now. We report case of primary retroperitoneal extra-ovarian SLCT in a seven-year girl child without any hormonal manifestation. She presented with complaint of left side abdominal swelling associated with intermittent pain for a duration of six months. CT scan revealed a huge retroperitoneal space-occupying lesion abutting the dorsal vertebrae and present posterior to pancreas, spleen and left kidney. The tumor was diagnosed as extraovarian Sertoli Leydig cell tumor with intermediate differentiation on histopathology and immunohistochemistry.
卵巢支持-间质细胞瘤（SLCT）占所有卵巢恶性肿瘤的比例不到0.5%。原发性卵巢外SLCT的发病率极其罕见，迄今为止报道的病例均发生在年轻成年女性中。我们报告了一例7岁女童原发性腹膜后卵巢外SLCT，无任何激素表现。她因左侧腹部肿胀伴间歇性疼痛6个月前来就诊。CT扫描显示一个巨大的腹膜后占位性病变，毗邻胸椎，位于胰腺、脾脏和左肾后方。经组织病理学和免疫组化检查，该肿瘤被诊断为中等分化的卵巢外支持-间质细胞瘤。
