Matyushkina A S, Gorbacheva A M, Tkachuk A V, Eremkina A K, Mokrysheva N G
Endocrinology Research Centre.
Probl Endokrinol (Mosk). 2022 Sep 19;68(6):59-66. doi: 10.14341/probl13159.
Primary hyperparathyroidism (PHPT) is a significant endocrine disease caused by increased production of parathyroid hormone (PTH) by altered parathyroid glands and violation of the mechanisms of regulation of serum calcium concentrations. These changes can lead to nephrolithiasis, osteoporosis, erosive and ulcerative lesions of the gastrointestinal tract, a number of less specific symptoms (nausea, vomiting, weakness, fatigue, etc.). Etiologically, in more than 85% of cases, PHPT is a consequence of sporadic solitary adenoma or hyperplasia parathyroid glands, however, in 1-3% of cases, the cause is carcinoma of parathyroid glands , including as part of various genetic syndromes. The importance of timely examination for PHPT of patients with characteristic clinical manifestations of this disease and - with an aggressive course - alertness towards carcinomas of parathyroid glands was noted. At the same time, the severity of the clinical picture and even the presence of suspicious signs characteristic of hereditary forms of carcinomas of parathyroid glands are not always a consequence of the malignant process. We present a description of a young patient with a severe course of PHPT, multiple fractures and a voluminous tumor of the upper jaw, developed as a result of a typical adenoma of parathyroid glands. Additionally, the algorithm of pre- and postoperative differential diagnosis for such patients is highlighted.
原发性甲状旁腺功能亢进症(PHPT)是一种重要的内分泌疾病,由甲状旁腺改变导致甲状旁腺激素(PTH)分泌增加以及血清钙浓度调节机制紊乱引起。这些变化可导致肾结石、骨质疏松、胃肠道糜烂和溃疡性病变以及一些不太特异的症状(恶心、呕吐、虚弱、疲劳等)。从病因学角度来看,超过85%的PHPT病例是散发性孤立性腺瘤或甲状旁腺增生的结果,然而,1%至3%的病例病因是甲状旁腺癌,包括作为各种遗传综合征的一部分。文中指出了对具有该疾病特征性临床表现的患者及时进行PHPT检查的重要性,以及对于病程进展迅速的患者要警惕甲状旁腺癌。与此同时,临床表现的严重程度甚至甲状旁腺癌遗传性形式的可疑体征的存在并不总是恶性病变的结果。我们描述了一名患有严重PHPT病程、多处骨折和上颌巨大肿瘤的年轻患者,该肿瘤是由典型的甲状旁腺腺瘤发展而来。此外,还强调了此类患者术前和术后鉴别诊断的算法。