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原发性卵巢滑膜肉瘤——病例报告

PRIMARY OVARIAN SYNOVIAL SARCOMA - A CASE REPORT.

作者信息

Yordanov A, Janeva K, Mateva S, Kornovski Y, Kostov S, Slavchev S, Ivanova Y, Nikolova M

机构信息

Department of Gynecologic Oncology, Medical University Pleven, Pleven 5800, Bulgaria.

Department of Gynecology, Saint Marina University Hospital, Pleven 5800, Bulgaria.

出版信息

Exp Oncol. 2022 Dec;44(4):334-336. doi: 10.32471/exp-oncology.2312-8852.vol-44-no-4.19072.

DOI:10.32471/exp-oncology.2312-8852.vol-44-no-4.19072
PMID:36811537
Abstract

Synovial sarcoma is an aggressive soft tissue sarcoma, which most often occurs in the limbs near the joints. It accounts for 5-10% of all soft tissue sarcomas. It extremely rarely affects the pelvis. So far, only 4 cases of primary involvement of the adnexa have been described. We present a case of a 77-year-old female patient diagnosed with a rapidly growing pelvic formation, subsequently diagnosed as monophasic synovial sarcoma of the ovary. Synovial sarcoma derived from the adnexa is a rare disease that is virtually unknown. The diagnosis is complex, and there is a poor prognosis.

摘要

滑膜肉瘤是一种侵袭性软组织肉瘤,最常发生于关节附近的四肢。它占所有软组织肉瘤的5%-10%。极少累及骨盆。迄今为止,仅报道过4例附件原发性受累的病例。我们报告一例77岁女性患者,其被诊断为盆腔肿物迅速增大,随后被诊断为卵巢单相滑膜肉瘤。起源于附件的滑膜肉瘤是一种极为罕见且几乎不为人知的疾病。诊断复杂,预后较差。

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