Department of Urology, The Affiliated Hospital of Zunyi Medical University, No.149 Dalian Road, Zunyi, Guizhou, China.
Department of Pathology, The Second Affiliated Hospital of Zunyi Medical University, Zunyi, Guizhou, China.
Diagn Pathol. 2023 Jul 3;18(1):78. doi: 10.1186/s13000-023-01367-z.
Synovial sarcoma (SS) is a rare malignant soft tissue sarcoma that originates from primitive mesenchymal cells with epithelial differentiation potential. It is most commonly found in the limbs and trunk. In the urinary system, it is mostly found in the kidneys. However, synovial sarcomas originating from the external urethra are extremely rare. Only one case of synovial sarcoma arising from the vulvar urethral orifice has been reported previously, and we report a second case of synovial sarcoma of the urethral orifice. In addition, a total of 16 vulvar synovial sarcomas were identified and the literature are analyzed in this report reviews from 1966 to the present.
滑膜肉瘤（SS）是一种罕见的恶性软组织肉瘤，起源于具有上皮分化潜能的原始间充质细胞。它最常见于四肢和躯干。在泌尿系统中，它主要发生在肾脏。然而，起源于外阴尿道外口的滑膜肉瘤极为罕见。以前仅报道过一例起源于外阴尿道外口的滑膜肉瘤，我们报告了第二例尿道外口滑膜肉瘤。此外，本报告共确定了 16 例外阴滑膜肉瘤，并对 1966 年至今的文献进行了回顾分析。
