Li Yalan, Zhou Han, Lu Ling, Dai Yanhong, Zhang Xiaoli, Chen Jie, Yu Chenjie, Qian Xiaoyun
Department of Otolaryngology Head and Neck Surgery,Nanjing Drum Tower Hospital,the Affiliated Hospital of Nanjing University Medical School,Jiangsu Provincial Key Medical Discipline,Research Institute of Otolaryngology,Nanjing,210008,China.
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2023 Mar;37(3):186-189;196. doi: 10.13201/j.issn.2096-7993.2023.03.006.
Congenital temporal bone cholesteatoma is a rare lesion in otolaryngology.The disease is locally invasive and may lead to significant complications,including hearing loss(conductive or sensorineural), temporal bone destruction and intracranial invasion. This article reviews the characteristic symptoms of congenital temporal bone cholesteatoma, testing and imaging of the disease, stage and the current treatment options in order to promote awareness to this rare disease entity and perform early surgical treatment, effectively avoid the destruction of the temporal bone and its surrounding structures, thereby reducing the occurrence of complications. By improving the understanding of the disease and performing early surgical treatment, the destruction of the temporal bone and its surrounding structures can be effectively avoided, thereby reducing the occurrence of complications.
先天性颞骨胆脂瘤是耳鼻喉科一种罕见的病变。该疾病具有局部侵袭性,可能导致严重并发症,包括听力损失(传导性或感音神经性)、颞骨破坏和颅内侵犯。本文综述了先天性颞骨胆脂瘤的特征性症状、该疾病的检查和影像学表现、分期以及当前的治疗选择,以提高对这种罕见疾病实体的认识并进行早期手术治疗,有效避免颞骨及其周围结构的破坏,从而减少并发症的发生。通过提高对该疾病的认识并进行早期手术治疗,可以有效避免颞骨及其周围结构的破坏,从而减少并发症的发生。