Thomas Rachel A, Warfield Dennis J, Nikkel Lucas E
Orthopaedic Surgery, Penn State Health Milton S. Hershey Medical Center, Hershey, PA, USA.
Anesthesiology and Perioperative Medicine, Penn State Health Milton S. Hershey Medical Center, Hershey, PA, USA.
Arthroplast Today. 2022 Nov 29;19:101021. doi: 10.1016/j.artd.2022.08.014. eCollection 2023 Feb.
Facioscapulohumeral dystrophy is an autosomal dominant disorder that results in progressive muscle weakness. Patients most commonly present with facial and periscapular muscle weakness, which progresses to involve their upper and lower extremities as well as truncal muscles. We present a patient with facioscapulohumeral dystrophy who underwent staged bilateral total hip arthroplasties but developed late prosthetic joint infection. This case also reports the management of periprosthetic joint infection after total hip arthroplasties through explant and placement of an articulating spacer as well as both neuraxial and general anesthetic management for this uncommon neuromuscular disorder.
面肩肱型肌营养不良症是一种常染色体显性疾病，会导致进行性肌肉无力。患者最常见的症状是面部和肩胛周围肌肉无力，随后逐渐发展至累及上肢、下肢以及躯干肌肉。我们报告了一例面肩肱型肌营养不良症患者，该患者接受了分期双侧全髋关节置换术，但术后发生了晚期人工关节感染。本病例还报告了全髋关节置换术后假体周围感染的处理方法，包括取出假体并放置关节间置器，以及针对这种罕见神经肌肉疾病的神经轴和全身麻醉管理。
