乳头肌弹力纤维瘤导致严重主动脉瓣狭窄。
Papillary fibroelastoma causing severe aortic stenosis.
作者信息
Yoshikai Masaru, Sato Hisashi, Hayashi Nagi, Kuwano Akito
机构信息
Department of Cardiovascular Surgery, Shin-Koga Hospital, Fukuoka, Japan.
出版信息
J Cardiol Cases. 2022 Dec 17;27(3):120-123. doi: 10.1016/j.jccase.2022.11.006. eCollection 2023 Mar.
UNLABELLED
Herein, we present a rare case of papillary fibroelastoma of the aortic valve, which caused severe aortic stenosis. The papillary fibroelastoma developed on the left ventricular side of the non-coronary cusp, immobilizing the cusp motion and obstructing the left ventricular outflow tract, resulting in severe aortic stenosis that brought on acute heart failure. The patient underwent an urgent surgical treatment, which resulted in a successful outcome. To the best of our knowledge, this is the first case of papillary fibroelastoma in which aortic stenosis was so severe as to cause congestive heart failure.
LEARNING OBJECTIVE
Papillary fibroelastoma (PFE) is the most commonly observed primary cardiac tumor in adults that commonly involves left heart chambers. While PFEs often cause embolisms, they rarely cause valvular dysfunction. In a case presented herein, a PFE developed on the left ventricular side of the non-coronary cusp, immobilizing the cusp motion and obstructing the left ventricular outflow tract, resulting in severe aortic stenosis that brought on acute heart failure.
未标注
在此，我们报告一例罕见的主动脉瓣乳头状纤维弹性瘤病例，该病例导致严重的主动脉瓣狭窄。乳头状纤维弹性瘤生长在无冠瓣的左心室侧，使瓣叶活动固定，并阻塞左心室流出道，导致严重的主动脉瓣狭窄，进而引发急性心力衰竭。患者接受了紧急手术治疗，手术成功。据我们所知，这是首例因乳头状纤维弹性瘤导致主动脉瓣狭窄严重至引起充血性心力衰竭的病例。
学习目标
乳头状纤维弹性瘤（PFE）是成人中最常见的原发性心脏肿瘤，常累及左心腔。虽然PFE常导致栓塞，但很少引起瓣膜功能障碍。在本文所报告的病例中，一个PFE生长在无冠瓣的左心室侧，使瓣叶活动固定，并阻塞左心室流出道，导致严重的主动脉瓣狭窄，进而引发急性心力衰竭。
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