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腔静脉后输尿管误诊一例;病例报告及文献复习

A missed diagnosis of retrocaval ureter; case report and review of the literature.

作者信息

Abduldaem Omar, Banihani Omaya, Alkeraithe Fawaz, Abasher Abdelazim

机构信息

Department of Urology, Armed Forced Hospital, Al-Kharj, Saudi Arabia.

Department of Pediatric Urology, King Saud Medical City, Riyadh, Saudi Arabia.

出版信息

Urol Case Rep. 2023 Feb 27;47:102364. doi: 10.1016/j.eucr.2023.102364. eCollection 2023 Mar.

Abstract

The retrocaval ureter is an uncommon congenital anomaly due to an abnormal development of the inferior vena cava. Our case describes an 8 year-old boy who was referred to our center as a case of ureteropelvic junction obstruction with persistent hydronephrosis after pyeloplasty. Retrograde pyelogram showed features of retrocaval ureter which was managed surgically with constructive repair of the ureter. The low clinical incidence may be due to a number of asymptomatic cases that are not diagnosed in the patient's lifetime.

摘要

腔静脉后输尿管是一种由于下腔静脉发育异常导致的罕见先天性畸形。我们的病例描述了一名8岁男孩,他因肾盂成形术后输尿管肾盂连接处梗阻伴持续性肾积水被转诊至我们中心。逆行肾盂造影显示了腔静脉后输尿管的特征,通过输尿管的结构性修复进行了手术治疗。临床发病率低可能是由于许多无症状病例在患者一生中未被诊断出来。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f8e6/10006511/16955393ecdf/gr1.jpg

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