Bi Zhaojun, Dong Peng, Sun Chunjuan, Shi Yinghong, Liu Jing, Ma Heng
Weifang Medical University, Weicheng District, Weifang, China.
Qingdao University Medical College Affiliated Yantai Yuhuangding Hospital, Yantai, China.
Arch Argent Pediatr. 2023 Dec 1;121(6):e202202853. doi: 10.5546/aap.2022-02853.eng. Epub 2023 Mar 23.
We reported a perineal lipoblastoma in a 5-year-old girl located in the right labia mayor. The lesion gradually increased within 6 months. Ultrasound and magnetic resonance imaging (MRI) showed a limited solid heterogenous tumor with fatty component. After it had been surgically removed, the anatomopathological examination confirmed that it was a lipoblastoma. Lipoblastoma is a rare benign mesenchymal tumor of infancy and early childhood. Symptoms vary depending on localization; signs of compression of adjacent organs may be seen. This type of unusual soft tissue tumors occurred most often in under 3 years old. The localization of lipoblastomas is predominantly in the extremities but may be also found in other sites including the head and neck, trunk, mediastinum, kidney, mesentery, retropritoneum and perineum. The suspicion should be considered according to ultrasound and MRI findings.
我们报告了一名5岁女童右侧大阴唇处的会阴脂肪母细胞瘤。该病变在6个月内逐渐增大。超声和磁共振成像（MRI）显示为一个边界清晰的实性异质性肿瘤，含有脂肪成分。手术切除后，解剖病理学检查证实为脂肪母细胞瘤。脂肪母细胞瘤是婴幼儿期罕见的良性间叶组织肿瘤。症状因部位而异；可能会出现邻近器官受压的体征。这类不寻常的软组织肿瘤最常发生于3岁以下儿童。脂肪母细胞瘤主要位于四肢，但也可见于其他部位，包括头颈部、躯干、纵隔、肾脏、肠系膜、腹膜后和会阴。应根据超声和MRI检查结果考虑诊断。
