Hoshimaru Takumi, Takagi Fugen, Tsuji Yuichiro, Yagi Ryokichi, Hiramatsu Ryo, Kameda Masahiro, Nonoguchi Naosuke, Furuse Motomasa, Kawabata Shinji, Takami Toshihiro, Wanibuchi Masahiko
Department of Neurosurgery, Osaka Medical and Pharmaceutical University, Takatsuki, Osaka, Japan.
NMC Case Rep J. 2023 Feb 23;10:27-32. doi: 10.2176/jns-nmc.2022-0346. eCollection 2023.
Primary germ cell tumors of the central nervous system (CNS) typically occur in the neurohypophysis, hypothalamus, or pineal gland and rarely in the spinal cord. We report a case of a spinal intramedullary tumor, which was first detected on magnetic resonance imaging (MRI) 41 months after the initial symptoms, with a verified pathological diagnosis of germinoma. The initial symptom was an abnormal sensation in the left plantar region that gradually worsened, resulting in severe sensory disturbance, difficulty in standing, and even bladder rectal disturbance. Repeated MRI after the onset failed to provide an imaging diagnosis. The MRI was performed 41 months after the onset and revealed a previously undiagnosed, contrast-enhancing spinal intramedullary neoplastic lesion at the Th11-12 level. Gross total resection of the tumor was successfully performed, and the pathology confirmed the diagnosis of pure germinoma. Postoperative chemotherapy, followed by local radiation, was successfully administered. Among primary germinomas of the CNS, occult germinoma that lacks imaging findings suggestive of tumors in the early stages of onset and becomes apparent over time is often reported as a primary neurohypophyseal germinoma, particularly in adolescents presenting with diabetes insipidus. In the present case, the lesion appeared to correspond to a primary occult germinoma of the intramedullary spinal cord.
中枢神经系统(CNS)的原发性生殖细胞肿瘤通常发生在神经垂体、下丘脑或松果体,很少发生在脊髓。我们报告一例脊髓髓内肿瘤病例,最初症状出现41个月后经磁共振成像(MRI)首次检测到,病理诊断为生殖细胞瘤。最初症状是左足底区域感觉异常,逐渐加重,导致严重感觉障碍、站立困难,甚至膀胱直肠功能障碍。发病后多次MRI检查均未能作出影像学诊断。发病41个月后进行MRI检查,发现胸11 - 12水平有一个先前未诊断出的、有强化的脊髓髓内肿瘤性病变。成功进行了肿瘤全切除,病理证实为纯生殖细胞瘤。术后成功进行了化疗,随后进行了局部放疗。在中枢神经系统原发性生殖细胞瘤中,隐匿性生殖细胞瘤在发病早期缺乏提示肿瘤的影像学表现,随时间推移才变得明显,常被报告为原发性神经垂体生殖细胞瘤,尤其是在患有尿崩症的青少年中。在本病例中,病变似乎符合脊髓髓内原发性隐匿性生殖细胞瘤。