Knani Leila, Werda Slim, Ghachem Mohamed, Mahjoub Anis
University of Sousse, Ibn Jazzar Medical School, Sousse, Tunisia.
Department of Ophthalmology, Farhat Hached University Hospital, Sousse, Tunisia.
Saudi J Ophthalmol. 2023 Mar 9;37(1):63-65. doi: 10.4103/sjopt.sjopt_9_21. eCollection 2023 Jan-Mar.
A 24-year-old woman presented for routine clinical evaluation. Her best-corrected visual acuity was 20/20 and slit-lamp examination of the anterior segment was normal in both eyes. Fundus examination of the left eye revealed a hypopigmented lesion, one disc diameter temporal to the fovea, with a hyperpigmented tail extending temporally from the main lesion, consistent with a torpedo maculopathy. Fundus autofluorescence showed an hypoautofluorescence with hyperautofluorescent border. Swept-source optical coherence tomography (OCT) showed a normal inner retina and a degeneration of the outer retina without retinal cavitation. OCT angiography (OCT-A) of the choriocapillaris layer revealed reverse shadowing caused by the increased transmission from the atrophied outer retina and RPE within the torpedo lesion and attenuation of signal in the area of the temporal hyperpigmentation. The superficial capillary plexus was normal. This case includes a multimodal imaging with OCT-A of torpedo maculopathy in a Tunisian woman. Further reports are required to provide a better understanding of this rare condition.
一名24岁女性前来进行常规临床评估。她的最佳矫正视力为20/20,双眼眼前节裂隙灯检查正常。左眼眼底检查发现一个色素减退性病变,位于黄斑中心凹颞侧一个视盘直径处,有一条色素沉着的尾巴从主要病变处向颞侧延伸,符合鱼雷样黄斑病变。眼底自发荧光显示低自发荧光伴高自发荧光边界。扫频光学相干断层扫描(OCT)显示视网膜内层正常,外层视网膜变性,无视网膜空洞形成。脉络膜毛细血管层的OCT血管造影(OCT-A)显示,鱼雷样病变内萎缩的外层视网膜和视网膜色素上皮(RPE)的透射增加导致反向阴影,颞侧色素沉着区域信号衰减。浅表毛细血管丛正常。该病例包括一名突尼斯女性鱼雷样黄斑病变的OCT-A多模态成像。需要更多报告以更好地了解这种罕见疾病。