Li Tiange, Ling Yunfei, Xiong Ziqing, An Qi
Department of Cardiovascular Surgery, West China Hospital of Sichuan University, Chengdu, China.
Front Cardiovasc Med. 2023 Mar 8;10:1071111. doi: 10.3389/fcvm.2023.1071111. eCollection 2023.
Unilateral absence of pulmonary artery (UAPA) is a rare type of congenital abnormality that may coexist with other congenital abnormalities or present as an isolated lesion, the latter form can be asymptomatic. Surgical procedure is usually carried out when UAPA was diagnosed with significant symptoms, and the aim of surgery is to restore the pulmonary flow distribution. The right-side UAPA is a considerable challenge for surgeons to process surgery, however, technical description of this type of UAPA are limited. Here we described a rare case of a two-month girl with absence of right pulmonary artery, we presented a technique that reconstructs this long-gap UAPA with contralateral pulmonary artery flap and autologous pericardial graft.
单侧肺动脉缺如（UAPA）是一种罕见的先天性异常，可与其他先天性异常并存或表现为孤立性病变，后一种形式可能无症状。当诊断出UAPA伴有明显症状时通常进行手术，手术目的是恢复肺血流分布。右侧UAPA对外科医生来说是一个巨大的手术挑战，然而，关于这种类型UAPA的技术描述有限。在此我们描述了一例罕见的两个月大女童右侧肺动脉缺如的病例，我们展示了一种用对侧肺动脉瓣和自体心包移植物重建这种长间隙UAPA的技术。
