经导管肝导管-奇静脉连接减少了一名青紫型Fontan患者的肺动静脉畸形。

Transcatheter Hepatic Conduit-Azygous Vein Connection Reduces Pulmonary Arteriovenous Malformations in a Cyanotic Fontan Patient.

作者信息

Ratnayaka Kanishka, Wei Zhenglun A, Ryan Justin R, Heyden Caitlin M, Narayan Hari K, Slesnick Timothy C, Lederman Robert J, Moore John W, Yoganathan Ajit P, El-Said Howaida G

机构信息

Department of Pediatric Cardiology, Rady Children's Hospital, University of California-San Diego, San Diego, California, USA.

Cardiovascular Branch, Division of Intramural Research, National Heart, Lung, and Blood Institute, Bethesda, Maryland, USA.

出版信息

JACC Case Rep. 2023 Mar 15;10:101760. doi: 10.1016/j.jaccas.2023.101760.

The authors report a closed-chest, transcatheter large-vessel connection (hepatic conduit to azygous vein) to reverse pulmonary arteriovenous malformations in a 10-year-old patient after Fontan for heterotaxy/interrupted inferior vena cava, with an increase in oxygen saturation from 78% to 96%. Computational fluid dynamics estimated a 14-fold increase in hepatic blood flow to the left pulmonary artery (from 1.3% to 14%). ().