Department of Vascular Surgery, Xuanwu Hospital, Capital Medical University, No. 45 Changchun Street, Xicheng District, 100053, Beijing, People's Republic of China.
Department of Vascular Interventional, Aerospace Central Hospital, No. 15 Yuquan Road, Haidian District, 100049, Beijing, People's Republic of China.
J Cardiothorac Surg. 2023 Apr 10;18(1):124. doi: 10.1186/s13019-023-02214-4.
Congenital portosystemic shunt (CPS) is a developmental anomaly of the portal vein system. The disease can cause blood from the portal vein to flow into the vena cava, resulting in various atypical clinical manifestations. Pelvic congestion syndrome (PCS) caused by CPS is particularly rare. A young woman with PCS had an abnormal communicating branch of the left ovarian vein (OV). Her left OV drained normally into the left renal vein, and at the same time communicated with the portal vein, forming an extrahepatic portosystemic shunt. With embolization of her left OV, the patient was cured of PCS.
先天性门体静脉分流（CPS）是门静脉系统发育异常。该疾病可导致门静脉中的血液流入腔静脉，引起各种非典型临床表现。CPS 引起的盆腔淤血综合征（PCS）特别罕见。一位年轻女性患有 PCS，其左侧卵巢静脉（OV）出现异常交通支。她的左侧 OV 正常排入左侧肾静脉，同时与门静脉相通，形成肝外门体分流。通过栓塞她的左侧 OV，该患者治愈了 PCS。
