Hailemariam Tesfahunegn, Demilew Endalew, Manyazewal Tsegahun, Sisay Samuel
Addis Ababa University, School of Medicine, Department of Radiology, 9080, Addis Ababa, Ethiopia.
Center for Innovative Drug Development and Therapeutic Trials for Africa (CDT-Africa), Addis Ababa University, College of Health Sciences, Addis Ababa, Ethiopia.
Radiol Case Rep. 2023 Jun 3;18(8):2750-2753. doi: 10.1016/j.radcr.2023.05.042. eCollection 2023 Aug.
Congenital portosystemic shunt (CPS) is a rare vascular anomaly resulting in diversion of splanchnic or portal blood into the systemic circulation. Other vascular malformations associated with this entity are uncommon. A 4-year-old female child with a diagnosis of acute viral hepatitis had an incidental finding of extrahepatic CPS on a Doppler abdominal ultrasound. Contrast-enhanced computed tomography showed a dilated portal vein having H-type side-to-side communication with a hypoplastic intrahepatic portion of the inferior vena cava and a prominent dilated azygos vein. There was retroaortic left renal vein drained into the IVC which was visualized in its entirety. Echocardiography findings were normal and the patient was discharged after symptomatic treatment that achieved improvement. With the expansion of abdominal imaging, incidental cases of CPS are increasingly being diagnosed in children. Although vascular malformations associated with CPS are rare, early diagnosis of cases helps avoid complications during shunt closure.
先天性门体分流（CPS）是一种罕见的血管异常，导致内脏或门静脉血分流至体循环。与此相关的其他血管畸形并不常见。一名诊断为急性病毒性肝炎的4岁女童在腹部多普勒超声检查时意外发现肝外CPS。增强计算机断层扫描显示门静脉扩张，与发育不全的肝内下腔静脉部分呈H型侧侧连通，奇静脉显著扩张。主动脉后左肾静脉引流至下腔静脉，全程可见。超声心动图检查结果正常，患者经对症治疗后症状改善出院。随着腹部影像学检查的普及，儿童CPS的偶然病例诊断越来越多。虽然与CPS相关的血管畸形很少见，但早期诊断有助于避免分流闭合时的并发症。
