Bhatia Harsimran, Bhatia Anmol, Saini Shiv Sajan, Kumar Rupesh, Sodhi Kushaljit Singh
Department of Radiodiagnosis and Imaging, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Department of Pediatrics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Ann Pediatr Cardiol. 2022 Sep-Dec;15(5-6):539-541. doi: 10.4103/apc.apc_217_21. Epub 2023 Mar 1.
Total anomalous pulmonary venous connection (TAPVC) is an uncommonly encountered cyanotic congenital heart disease characterized by anomalous drainage of the pulmonary veins. Concomitant venous anomalies are rarely found in these patients. We present a case of an infra-cardiac TAPVC with an intrahepatic portosystemic shunt, where a vascular channel was seen between the middle hepatic vein and the left branch of the portal vein with fusiform dilatation of the latter, diagnosed on computed tomography angiography.
完全性肺静脉异位连接(TAPVC)是一种罕见的青紫型先天性心脏病,其特征为肺静脉引流异常。这些患者很少同时发现静脉异常。我们报告一例心下型TAPVC合并肝内门体分流的病例,在计算机断层血管造影中发现肝中静脉与门静脉左支之间存在一个血管通道,后者呈梭形扩张。