IRCCS Fondazione Don Carlo Gnocchi ONLUS, Milan, Italy.
J Alzheimers Dis. 2023;93(4):1237-1276. doi: 10.3233/JAD-221279.
Alzheimer's disease starts in neural stem cells (NSCs) in the niches of adult neurogenesis. All primary factors responsible for pathological tau hyperphosphorylation are inherent to adult neurogenesis and migration. However, when amyloid pathology is present, it strongly amplifies tau pathogenesis. Indeed, the progressive accumulation of extracellular amyloid-β deposits in the brain triggers a state of chronic inflammation by microglia. Microglial activation has a significant pro-neurogenic effect that fosters the process of adult neurogenesis and supports neuronal migration. Unfortunately, this "reactive" pro-neurogenic activity ultimately perturbs homeostatic equilibrium in the niches of adult neurogenesis by amplifying tau pathogenesis in AD. This scenario involves NSCs in the subgranular zone of the hippocampal dentate gyrus in late-onset AD (LOAD) and NSCs in the ventricular-subventricular zone along the lateral ventricles in early-onset AD (EOAD), including familial AD (FAD). Neuroblasts carrying the initial seed of tau pathology travel throughout the brain via neuronal migration driven by complex signals and convey the disease from the niches of adult neurogenesis to near (LOAD) or distant (EOAD) brain regions. In these locations, or in close proximity, a focus of degeneration begins to develop. Then, tau pathology spreads from the initial foci to large neuronal networks along neural connections through neuron-to-neuron transmission.
阿尔茨海默病始于成年神经发生龛中的神经干细胞 (NSC)。所有导致病理性 tau 过度磷酸化的主要因素都固有存在于成年神经发生和迁移中。然而,当淀粉样蛋白病理学存在时,它会强烈放大 tau 发病机制。事实上,脑内细胞外淀粉样蛋白-β 沉积物的进行性积累会通过小胶质细胞引发慢性炎症状态。小胶质细胞的激活具有显著的促神经发生作用,促进成年神经发生过程并支持神经元迁移。不幸的是,这种“反应性”促神经发生活性最终通过放大 AD 中的 tau 发病机制扰乱了成年神经发生龛中的内稳态平衡。这种情况涉及到迟发性 AD(LOAD)中海马齿状回颗粒下区的 NSCs 和早发性 AD(EOAD)中沿侧脑室的脑室-室下区的 NSCs,包括家族性 AD(FAD)。携带 tau 病理学初始种子的神经前体细胞通过复杂信号驱动的神经元迁移在整个大脑中迁移,并将疾病从成年神经发生龛传播到邻近(LOAD)或遥远(EOAD)的脑区。在这些位置或附近,开始出现退化焦点。然后,tau 病理学通过神经元到神经元的传递沿着神经连接从初始焦点扩散到大型神经元网络。