College of Medicine, Neurosurgery, Imam Abdulrahman Bin Faisal University, Saudi Arabia.
Neurosurgery, King Fahd University Hospital, Imam Abdulrahman Bin Faisal University, Saudi Arabia.
Med Arch. 2023 Apr;77(2):150-154. doi: 10.5455/medarh.2023.77.150-154.
Myxopapillary ependymoma is a rare type of primary spinal tumor, it is distinctly a slow-growing tumor that originates in the conus medullaris, cauda equina, or film terminals and is rarely identified as a multicentric type. Myxopapillary ependymoma has a unique histological characteristic and is associated with a generally better prognosis.
We present a case of a rare multicentric myxopapillary ependymoma.
A 28-year-old male with 1-year history of low back pain and 3 months of radiating pain to left lower limb with perianal anesthesia. Magnetic resonance imaging (MRI) exhibited a large intradural intramedullary lesion from the level of the conus medullaris extending to the filum terminals at the level of T12 to L3 with smaller multiple enhancing lesions seen opposite to L4 and L5 level as well as within the exiting nerve roots, at the left side of L1/L2 and L2/L3 and right side of L3/L4 and L5/S1 level. The patient underwent surgical resection with significant improvement in symptoms and no tumor progression on follow up MRI scan.
We hereby present a case of multicentric myxopapillary ependymoma with a literature review of the previous reported cases. We believe that our study will make a significant contribution to the literature and will be of interest to the readership regarding of the rarity of multicentric Myxopapillary ependymoma and it will help in decision making for the proper surgical Intervention on these kinds of cases.
黏液乳头状室管膜瘤是一种罕见的原发性脊髓肿瘤，它是一种明显的缓慢生长的肿瘤，起源于脊髓圆锥、马尾或终丝，很少被认为是多中心型。黏液乳头状室管膜瘤具有独特的组织学特征，预后一般较好。
我们报告一例罕见的多中心黏液乳头状室管膜瘤病例。
一名 28 岁男性，病史 1 年，表现为腰痛，3 个月来出现左下肢放射痛，伴有肛周麻醉。磁共振成像（MRI）显示从脊髓圆锥水平延伸至 T12 至 L3 水平的硬脊膜内髓内大病变，伴有多个较小的增强病变，位于 L4 和 L5 水平以及相应神经根内，L1/L2 和 L2/L3 左侧、L3/L4 和 L5/S1 右侧。患者接受了手术切除，症状显著改善，随访 MRI 扫描未见肿瘤进展。
我们报告了一例多中心黏液乳头状室管膜瘤病例，并对以往报道的病例进行了文献复习。我们相信，我们的研究将对文献做出重要贡献，并引起读者的兴趣，因为多中心黏液乳头状室管膜瘤罕见，这将有助于对这类病例进行适当的手术干预决策。
