Li Ting, Wang Haoru, Chen Xin, He Ling
Department of Radiology, Children's Hospital of Chongqing Medical University, National Clinical Research Center for Child Health and Disorders, Ministry of Education Key Laboratory of Child Development and Disorders, Chongqing Key Laboratory of Pediatrics, Chongqing, China.
Front Pediatr. 2023 May 23;11:1161603. doi: 10.3389/fped.2023.1161603. eCollection 2023.
Retroperitoneal extrarenal Wilms tumor is a rare condition in children that can be easily misdiagnosed as other retroperitoneal malignancies unrelated to the renal origin. Computerized tomography scan plays a crucial role in diagnosing and distinguishing retroperitoneal malignancies. In this report, we present two cases of retroperitoneal extrarenal Wilms tumor in children who were admitted due to abdominal mass. Laboratory examination did not reveal any significant abnormality. However, a computerized tomography scan revealed a solid or cystic-solid mass in the retroperitoneum accompanied by a bone spur extending from the anterior edge of the vertebral body to the back of the mass, while the origin of the tumor remained unclear. By analyzing these two cases and reviewing previous studies on retroperitoneal extrarenal Wilms tumor in children, we summarized the clinical and imaging characteristics of this rare condition. We also found that the presence of a spinal deformity adjacent to the mass might indicate the possibility of a retroperitoneal extrarenal Wilms tumor.
腹膜后肾外威尔姆斯瘤在儿童中是一种罕见病症，很容易被误诊为与肾脏起源无关的其他腹膜后恶性肿瘤。计算机断层扫描在诊断和鉴别腹膜后恶性肿瘤方面起着关键作用。在本报告中，我们呈现了两例因腹部肿块入院的儿童腹膜后肾外威尔姆斯瘤病例。实验室检查未发现任何显著异常。然而，计算机断层扫描显示腹膜后有一个实性或囊实性肿块，伴有一个从椎体前缘延伸至肿块后方的骨赘，而肿瘤的起源仍不明确。通过分析这两例病例并回顾以往关于儿童腹膜后肾外威尔姆斯瘤的研究，我们总结了这种罕见病症的临床和影像学特征。我们还发现，肿块附近存在脊柱畸形可能提示腹膜后肾外威尔姆斯瘤的可能性。
