肾外威尔姆斯瘤

Extrarenal Wilms' tumour.

作者信息

Suzuki K, Miyake H, Tashiro M, Mori H, Fukushige T, Tanimura R, Yokoyama S

机构信息

Department of Radiology, Oita Medical University, Japan.

出版信息

Pediatr Radiol. 1993;23(2):149-50. doi: 10.1007/BF02012413.

DOI:10.1007/BF02012413

PMID:8390643

Abstract

Extrarenal Wilms' tumour is rare and its imaging has received scant mention in the literature. We describe a 2-year-old boy with a firm mass in the right flank. CT, MRI and ultrasonography showed an inhomogeneous solid mass located in the retroperitoneum, which was separate from the right kidney. Angiography showed an enlarged right gonadal artery and irregularly tortuous vessels in the tumour similar to intrarenal Wilms' tumour ("spider leg" or "creeping vine" appearance). Histopathological examination confirmed an extrarenal Wilms' tumour.

摘要

肾外威尔姆斯瘤罕见，其影像学表现鲜有文献提及。我们报告一名2岁男性患儿，右侧腹可触及一质地坚硬的肿块。CT、MRI及超声检查显示，一不均匀实性肿块位于腹膜后，与右肾分离。血管造影显示右侧性腺动脉增粗，肿瘤内血管呈不规则迂曲，类似肾内威尔姆斯瘤（“蜘蛛腿”或“蔓状”表现）。组织病理学检查确诊为肾外威尔姆斯瘤。