Li Yanan, Lei Chuanfen, Xiang Bo, Li Fuyu, Wang Chuan, Wang Qi, Chen Siyuan, Ji Yi
aDivision of Oncology, Department of Pediatric Surgery bDepartment of Pathology cPediatric Intensive Care Unit, West China Hospital of Sichuan University, Chengdu, China.
Medicine (Baltimore). 2017 Nov;96(46):e8670. doi: 10.1097/MD.0000000000008670.
Teratoma with nephroblastoma is a rare disease. The most common site at which teratoma with nephroblastoma occurs is the kidney. The mechanisms underlying the development of teratoma with nephroblastoma have not been fully elucidated.
In the current report, we describe the clinical characteristics of a 3-year-old girl with a complaint of a painless abdominal mass in the upper right side of the body. Ultrasonography and computed tomography revealed a cystic-solid mass with a clear boundary.
Surgical resection and a subsequent pathological examination confirmed that the mass contained teratoma tissues and renal blastemal components, which supports the diagnosis of teratoma with nephroblastoma.
The patient underwent an exploratory laparotomy through a transverse abdominal incision. Complete resection of the mass was performed in this patient.
The patient's postoperative course was uneventful and she was discharged on the 8th postoperative day. The girl had no complaints during the 2 years follow-up period.
Teratoma with nephroblastoma is a rare entity that typically presents in childhood. Due to its rarity, no standardized criteria have been established for the categorization and treatment of these lesions. However, a complete excision of this tumor allows the diagnosis to be confirmed and lowers the risk of recurrence.
肾母细胞瘤合并畸胎瘤是一种罕见疾病。肾母细胞瘤合并畸胎瘤最常见的发生部位是肾脏。肾母细胞瘤合并畸胎瘤的发病机制尚未完全阐明。
在本报告中，我们描述了一名3岁女孩的临床特征，她主诉身体右上腹有一个无痛性腹部肿块。超声检查和计算机断层扫描显示为一个边界清晰的囊实性肿块。
手术切除及随后的病理检查证实肿块包含畸胎瘤组织和肾母细胞成分，这支持了肾母细胞瘤合并畸胎瘤的诊断。
患者通过腹部横切口接受了剖腹探查术。对该患者进行了肿块的完整切除。
患者术后恢复顺利，术后第8天出院。在2年的随访期内，该女孩无不适主诉。
肾母细胞瘤合并畸胎瘤是一种罕见的疾病，通常在儿童期出现。由于其罕见性，尚未建立针对这些病变分类和治疗的标准化标准。然而，完整切除该肿瘤可确诊并降低复发风险。
