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法洛四联症合并主动脉狭窄及共同动脉干:是否存在形态学上的重叠?

Tetralogy of Fallot with aortic stenosis and common arterial trunk: Is there a morphological overlap?

作者信息

Kakarla Saikiran, Sasikumar Deepa, Ayyappan Anoop

机构信息

Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, Kerala, India.

Department of Imaging Sciences and Intervention Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, Kerala, India.

出版信息

Ann Pediatr Cardiol. 2023 Jan-Feb;16(1):61-64. doi: 10.4103/apc.apc_81_22. Epub 2023 Apr 4.

DOI:10.4103/apc.apc_81_22
PMID:37287845
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10243663/
Abstract

Tetralogy of Fallot with aortic stenosis is an extremely rare entity which bears some morphological similarities with the common arterial trunk. Through two illustrative cases of TOF with aortic stenosis we describe the shared anatomical peculiarities of the two anomalies with a review of the possible genetic and developmental factors responsible for the association.

摘要

法洛四联症合并主动脉狭窄是一种极其罕见的病症,它与共同动脉干在形态上有一些相似之处。通过两例法洛四联症合并主动脉狭窄的病例,我们描述了这两种异常情况共有的解剖学特点,并回顾了可能导致这种关联的遗传和发育因素。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/93e9/10243663/ef36acde8114/APC-16-61-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/93e9/10243663/2dac1b5827bb/APC-16-61-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/93e9/10243663/ef36acde8114/APC-16-61-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/93e9/10243663/2dac1b5827bb/APC-16-61-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/93e9/10243663/ef36acde8114/APC-16-61-g002.jpg

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1
Tetralogy of Fallot with aortic stenosis and common arterial trunk: Is there a morphological overlap?法洛四联症合并主动脉狭窄及共同动脉干:是否存在形态学上的重叠?
Ann Pediatr Cardiol. 2023 Jan-Feb;16(1):61-64. doi: 10.4103/apc.apc_81_22. Epub 2023 Apr 4.
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本文引用的文献

1
Tetralogy of Fallot with aortic stenosis: repair without aortic valve intervention.
Pediatr Cardiol. 2009 Oct;30(7):1019-21. doi: 10.1007/s00246-009-9480-8. Epub 2009 Jun 4.
2
Tetralogy of Fallot with congenital aortic valvar stenosis: the tetralogy-truncus interrelationship.法洛四联症合并先天性主动脉瓣狭窄:四联症与共同动脉干的相互关系。
Pediatr Cardiol. 2006 May-Jun;27(3):354-9. doi: 10.1007/s00246-005-1182-2.
3
Tetralogy of Fallot with aortic valvular stenosis and deletion 22q11.
Ann Thorac Surg. 2003 Jun;75(6):2010-1; author reply 2011. doi: 10.1016/s0003-4975(02)04671-4.
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Tetralogy of Fallot with aortic valvular stenosis: surgical correction in one case.法洛四联症合并主动脉瓣狭窄:1例手术矫正
Ann Thorac Surg. 2002 Mar;73(3):967-9. doi: 10.1016/s0003-4975(01)03017-x.
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Malformations of the aortic valve in patients with the tetralogy of Fallot.法洛四联症患者的主动脉瓣畸形
Am Heart J. 1968 Dec;76(6):755-9. doi: 10.1016/0002-8703(68)90260-3.
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Truncal or aortic valve stenosis in functionally single arterial trunk. A clinical, hemodynamic and pathologic study of six cases.功能性单一大动脉干中的躯干或主动脉瓣狭窄。6例临床、血流动力学及病理学研究。
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