Department of Rheumatology and Immunology, Fujian Provincial Hospital, Shengli Clinical Medical College of Fujian Medical University, Fuzhou, China.
Department of Radiology, China-Japan Friendship Hospital, Beijing, China.
Front Immunol. 2023 May 23;14:1194721. doi: 10.3389/fimmu.2023.1194721. eCollection 2023.
Pneumatosis cystoides intestinalis (PCI) in adult dermatomyositis (DM) is rarely described. This report aimed to describe the clinical features and prognosis of PCI in six adult patients with DM (four with anti-MDA5 antibodies, one with anti-SAE antibodies, and one with anti-TIF-1γ antibodies). Except for one patient with transient abdominal pain, the remaining five patients were asymptomatic. PCI occurred in the ascending colon in all patients, of whom five had free gas in the abdominal cavity. No patients received excessive treatment, and PCI disappeared in four patients during the follow-up. Additionally, we reviewed previous studies on this complication.
肠囊样积气（PCI）在成人皮肌炎（DM）中很少见。本报告旨在描述 6 例成人 DM 合并 PCI 的临床特征和预后（4 例抗 MDA5 抗体阳性，1 例抗 SAE 抗体阳性，1 例抗 TIF-1γ 抗体阳性）。除 1 例患者有短暂腹痛外，其余 5 例患者均无症状。所有患者的 PCI 均发生在升结肠，其中 5 例患者有腹腔游离气体。无患者接受过度治疗，4 例患者在随访中 PCI 消失。此外，我们还对该并发症的以往研究进行了回顾。
