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Not All Heme is "Free" in Sickle Cell Disease.

作者信息

Vinchi Francesca

机构信息

Iron Research Laboratory, Lindsley Kimball Research Institute, New York Blood Center, NY, USA.

Department of Pathology and Laboratory Medicine, Weill Cornell Medicine, NY, USA.

出版信息

Hemasphere. 2023 Jun 19;7(7):e910. doi: 10.1097/HS9.0000000000000910. eCollection 2023 Jul.

DOI:10.1097/HS9.0000000000000910
PMID:37346451
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10281323/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/11cc/10281323/511ca90d5411/hs9-7-e910-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/11cc/10281323/511ca90d5411/hs9-7-e910-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/11cc/10281323/511ca90d5411/hs9-7-e910-g001.jpg

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本文引用的文献

1
Sickle red blood cell-derived extracellular vesicles activate endothelial cells and enhance sickle red cell adhesion mediated by von Willebrand factor.镰状红细胞衍生的细胞外囊泡激活血管内皮细胞,并增强血管性血友病因子介导的镰状红细胞黏附。
Br J Haematol. 2023 May;201(3):552-563. doi: 10.1111/bjh.18616. Epub 2023 Jan 5.
2
Extracellular Vesicles in Sickle Cell Disease: A Promising Tool.镰状细胞病中的细胞外囊泡:一种有前景的工具。
Bioengineering (Basel). 2022 Sep 5;9(9):439. doi: 10.3390/bioengineering9090439.
3
Vasculo-toxic and pro-inflammatory action of unbound haemoglobin, haem and iron in transfusion-dependent patients with haemolytic anaemias.
依赖输血的溶血性贫血患者中未结合血红蛋白、血红素和铁的血管毒性和促炎作用。
Br J Haematol. 2021 May;193(3):637-658. doi: 10.1111/bjh.17361. Epub 2021 Mar 15.
4
Hemopexin therapy reverts heme-induced proinflammatory phenotypic switching of macrophages in a mouse model of sickle cell disease.血红素结合蛋白疗法可逆转镰状细胞病小鼠模型中血红素诱导的巨噬细胞促炎表型转换。
Blood. 2016 Jan 28;127(4):473-86. doi: 10.1182/blood-2015-08-663245. Epub 2015 Dec 16.
5
Circulating cell membrane microparticles transfer heme to endothelial cells and trigger vasoocclusions in sickle cell disease.循环细胞膜微粒将血红素转移至内皮细胞并引发镰状细胞病中的血管阻塞。
Blood. 2015 Jun 11;125(24):3805-14. doi: 10.1182/blood-2014-07-589283. Epub 2015 Mar 31.
6
Heme on innate immunity and inflammation.血红素与固有免疫和炎症
Front Pharmacol. 2014 May 27;5:115. doi: 10.3389/fphar.2014.00115. eCollection 2014.
7
Heme triggers TLR4 signaling leading to endothelial cell activation and vaso-occlusion in murine sickle cell disease.亚铁血红素触发 TLR4 信号通路,导致小鼠镰状细胞病中的内皮细胞激活和血管阻塞。
Blood. 2014 Jan 16;123(3):377-90. doi: 10.1182/blood-2013-04-495887. Epub 2013 Nov 25.
8
Therapeutic approaches to limit hemolysis-driven endothelial dysfunction: scavenging free heme to preserve vasculature homeostasis.限制溶血导致的内皮功能障碍的治疗方法:清除游离血红素以维持血管内环境稳定。
Oxid Med Cell Longev. 2013;2013:396527. doi: 10.1155/2013/396527. Epub 2013 May 27.