Department of Pediatrics, Kyoto City Hospital, Kyoto, Japan.
Department of Pediatrics, Okayama University Hospital, Okayama, Japan.
Int J Hematol. 2023 Sep;118(3):364-373. doi: 10.1007/s12185-023-03626-7. Epub 2023 Jun 26.
Hematopoietic stem cell transplantation (HSCT) is only indicated for acute lymphoblastic leukemia (ALL) patients for whom other treatments are unlikely to be curative. However, outcomes of patients not in complete remission (CR) at HSCT remain very poor. To improve the outcomes of patients receiving HSCT, it is important to obtain detailed clinical information about patients with ALL receiving HSCT in CR and not in CR. Patients enrolled in the Japan Association of Childhood Leukemia Study ALL-02 who underwent HSCT and were not in CR (non-CR patients, n = 55) were examined. The 1-year overall survival (OS) rate of non-CR patients was 27.3%. Compared with CR patients, non-CR patients experienced very early and early relapse significantly more frequently and had poorer prognostic factors. Most interestingly, high hyperdiploid (HHD) patients showed an excellent 1-year OS of 80%. In addition, long-term survival among surviving HHD patients was longer than 5 years. All eight patients who survived after undergoing HSCT while not in CR were younger than 10 years at initial diagnosis and were negative for central nervous system involvement. While limited, these results suggest that a subset of patients may benefit from HSCT while not in CR.
造血干细胞移植(HSCT)仅适用于其他治疗方法不太可能治愈的急性淋巴细胞白血病(ALL)患者。然而,未在 HSCT 时达到完全缓解(CR)的患者的预后仍然非常差。为了改善接受 HSCT 的患者的预后,重要的是获得关于在 CR 和非 CR 时接受 HSCT 的 ALL 患者的详细临床信息。对接受 HSCT 且未达到 CR(非 CR 患者,n=55)的日本儿童白血病研究协会 ALL-02 患者进行了检查。非 CR 患者的 1 年总生存率(OS)为 27.3%。与 CR 患者相比,非 CR 患者明显更早且更频繁地出现早期复发,并且预后因素较差。最有趣的是,高倍体(HHD)患者的 1 年 OS 率高达 80%。此外,存活的 HHD 患者的长期生存时间超过 5 年。在非 CR 时接受 HSCT 后存活的所有 8 名患者的初始诊断时年龄均小于 10 岁,且无中枢神经系统受累。尽管有限,但这些结果表明,某些患者可能会从非 CR 时的 HSCT 中受益。