Epithelioid angiosarcoma of the adrenal gland with metastasis: a case report and literature review.

UNLABELLED

Primary adrenal epithelioid angiosarcoma is an exceptionally rare condition, with only 51 cases reported in the literature since 1988.

CASE PRESENTATION

We report a case of a 59-year-old male patient who presented with a 4-month history of left flank pain and anemia. Radiographic imaging identified a 14 cm mass lesion in the left suprarenal region, which showed heterogeneous enhancement. The patient underwent total adrenalectomy with tumor-free surgical margins. Histological sections showed features consistent with an epithelioid tumor, and immunohistochemical staining confirmed the diagnosis of epithelioid angiosarcoma of the left adrenal gland.

DISCUSSION

Primary adrenal epithelioid angiosarcoma is a very rare entity. It was first described by Kareti in 1998. The most common presentation is an abdominal mass associated with pain. As there are no specific imaging findings for this tumor, histology combined with immunohistochemistry is the most definitive diagnostic method. Surgery with adjuvant chemotherapy is the management reported for previous cases.

CONCLUSION

In cases of rare malignancies, interdisciplinary collaboration is crucial for determining the optimal management strategy.