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解开肥厚型心肌病心源性猝死之谜:心脏磁共振成像的额外作用

Solving the Riddle of Sudden Cardiac Death in Hypertrophic Cardiomyopathy: The Added Role of Cardiac Magnetic Resonance.

作者信息

Stankowski Kamil, Figliozzi Stefano, Lisi Costanza, Catapano Federica, Panico Cristina, Cannata Francesco, Mantovani Riccardo, Frontera Antonio, Bragato Renato Maria, Stefanini Giulio, Monti Lorenzo, Condorelli Gianluigi, Francone Marco

机构信息

Department of Biomedical Sciences, Humanitas University, Via Rita Levi Montalcini, 4, Pieve Emanuele, 20090 Milano, Italy.

Humanitas Research Hospital IRCCS, Via Alessandro Manzoni, 56, Rozzano, 20089 Milano, Italy.

出版信息

J Cardiovasc Dev Dis. 2023 May 23;10(6):226. doi: 10.3390/jcdd10060226.

Abstract

Cardiac magnetic resonance (CMR) has been recently implemented in clinical practice to refine the daunting task of establishing the risk of sudden cardiac death (SCD) in patients with hypertrophic cardiomyopathy (HCM). We present an exemplificative case highlighting the practical clinical utility of this imaging modality in a 24-year-old man newly diagnosed with an apical HCM. CMR was essential in unmasking a high risk of SCD, which appeared low-intermediate after traditional risk assessment. A discussion examines the essential role of CMR in guiding the patient's therapy and underlines the added value of CMR, including novel and potential CMR parameters, compared to traditional imaging assessment for SCD risk stratification.

摘要

心脏磁共振成像(CMR)最近已应用于临床实践,以完善在肥厚型心肌病(HCM)患者中确定心脏性猝死(SCD)风险这一艰巨任务。我们展示了一个典型病例,突出了这种成像方式在一名新诊断为心尖部HCM的24岁男性患者中的实际临床应用价值。CMR对于揭示SCD的高风险至关重要,而在传统风险评估后该风险看似为低至中度。本文通过讨论审视了CMR在指导患者治疗中的重要作用,并强调了CMR相较于传统成像评估在SCD风险分层方面的附加价值,包括新的和潜在的CMR参数。

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