Roberts J A, Tullett W M, Thomas J S, Galloway D, Stack B H
Scott Med J. 1986 Apr;31(2):109. doi: 10.1177/003693308603100210.
Cystic fibrosis (CF) is an autosomal recessive condition affecting one in 2,000 live births in the UK. There are few reports of malignant tumours in this condition probably because, until recently, the majority died before the age of 30 years as a result of recurrent and chronic bronchopulmonary infection with impaired growth and development and resistance to infection due to pancreatic malabsorption. We describe an adult male with CF who died from an adenocarcinoma affecting the ileocaecal region of the bowel.
囊性纤维化（CF）是一种常染色体隐性疾病，在英国每2000例活产儿中就有1例受其影响。关于这种疾病合并恶性肿瘤的报道很少，可能是因为直到最近，大多数患者由于反复慢性支气管肺部感染、生长发育受损以及胰腺吸收不良导致抗感染能力下降，在30岁之前就去世了。我们报告一例成年男性囊性纤维化患者，其死于累及回盲部的腺癌。
