Jari Mohsen, Nasiri Shidrokh, Ghandehari Mohammadreza
Department of Pediatric Rheumatology, Imam Hossein Children's Hospital, Isfahan University of Medical Sciences, Isfahan, Iran.
School of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran.
SAGE Open Med Case Rep. 2023 Jun 29;11:2050313X231182237. doi: 10.1177/2050313X231182237. eCollection 2023.
Behçet's disease is a chronic multisystem vasculitis that presented with several manifestations. Episcleritis is a benign inflammation of the episcleral tissue and is rarely reported in Behçet's disease. We reported an 11-year-old girl who was admitted due to pain and swelling around the left eye with initial diagnosis of preseptal cellulitis. The patient had a history of recurrent oral aphthous ulcers and genital ulcers. Episcleritis and posterior uveitis were reported in ophthalmic examination and ultrasonography. Pathergy skin test and human leukocyte antigens (HLA) B5 and HLA-B51 were positive, consistent with the diagnosis of Behcet's disease. This case report emphasizes that various pathological causes may cause episcleritis and uveitis in children, one of which is rheumatic diseases, that should always be considered.
白塞病是一种慢性多系统血管炎,有多种表现形式。巩膜表层炎是巩膜组织的良性炎症,在白塞病中很少有报道。我们报告了一名11岁女孩,因左眼周围疼痛和肿胀入院,初步诊断为睑前蜂窝织炎。该患者有复发性口腔溃疡和生殖器溃疡病史。眼科检查和超声检查发现巩膜表层炎和后葡萄膜炎。针刺反应皮肤试验以及人类白细胞抗原(HLA)B5和HLA - B51呈阳性,符合白塞病的诊断。本病例报告强调,多种病理原因可能导致儿童巩膜表层炎和葡萄膜炎,其中之一是风湿性疾病,应始终予以考虑。