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本文引用的文献

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Fetal Non-Ovarian Abdominopelvic Cystic Lesions: A Single-Center Report.胎儿非卵巢腹盆腔囊性病变:单中心报告。
Fetal Diagn Ther. 2020;47(12):955-959. doi: 10.1159/000510814. Epub 2020 Oct 13.
2
Personalized medicine in chronic kidney disease by detection of monogenic mutations.遗传性肾脏疾病的个体化医学:单基因突变检测。
Nephrol Dial Transplant. 2020 Mar 1;35(3):390-397. doi: 10.1093/ndt/gfz028.
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Fetal abdominal cysts: antenatal course and postnatal outcomes.胎儿腹部囊肿:产前病程和产后结局。
J Perinat Med. 2019 May 27;47(4):418-421. doi: 10.1515/jpm-2018-0311.
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Magnetic resonance imaging of fetal pelvic cysts.胎儿盆腔囊肿的磁共振成像。
Abdom Radiol (NY). 2016 Dec;41(12):2445-2454. doi: 10.1007/s00261-016-0980-8.
5
Clinical Implications of Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome in the Prepubertal Age Group.青春期前年龄组梗阻性半阴道并同侧肾异常(OHVIRA)综合征的临床意义
PLoS One. 2016 Nov 18;11(11):e0166776. doi: 10.1371/journal.pone.0166776. eCollection 2016.
6
OHVIRA: Uterus didelphys, blind hemivagina and ipsilateral renal agenesis: Advantage MRI.OHVIRA:双子宫、盲端半阴道和同侧肾缺如:MRI的优势
J Hum Reprod Sci. 2012 Jan;5(1):67-70. doi: 10.4103/0974-1208.97811.
7
Multicystic dysplastic kidney disease presenting with a single large cyst in a fetus-anatomical basis and radiological aspects.多囊性发育不良肾脏疾病在胎儿中表现为单个大囊肿——解剖学基础和影像学表现。
Pediatr Neonatol. 2011 Aug;52(4):227-31. doi: 10.1016/j.pedneo.2011.05.009. Epub 2011 Jun 11.
8
Antenatally diagnosed giant multicystic dysplastic kidney resected during the neonatal period.产前诊断为巨大多囊性发育不良肾,于新生儿期行肾切除术。
J Pediatr Surg. 2008 Nov;43(11):2118-20. doi: 10.1016/j.jpedsurg.2008.07.010.
9
Comparison of magnetic resonance urography with ultrasound studies in detection of fetal urogenital anomalies.磁共振尿路造影与超声检查在胎儿泌尿生殖系统异常检测中的比较。
J Pediatr Urol. 2008 Feb;4(1):32-9. doi: 10.1016/j.jpurol.2007.07.005. Epub 2007 Sep 20.
10
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: management and follow-up.梗阻性半阴道与同侧肾异常(OHVIRA)综合征:管理与随访
Fertil Steril. 2007 Apr;87(4):918-22. doi: 10.1016/j.fertnstert.2006.11.015. Epub 2007 Feb 22.

一例表现为单个中线盆腔囊肿的多囊性发育不良肾病例。

A Case of Multicystic Dysplastic Kidney Presenting as a Single Midline Pelvic Cyst.

作者信息

Ebert Kristin M, Ching Christina B

机构信息

Division of Urology, Nationwide Children's Hospital, Columbus, OH, USA.

出版信息

Case Rep Nephrol Dial. 2023 Jul 4;13(1):57-62. doi: 10.1159/000530925. eCollection 2023 Jan-Dec.

DOI:10.1159/000530925
PMID:37484796
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10359676/
Abstract

We present an unusual case of a female neonate presenting with a single midline pelvic cyst. Prenatal imaging was suggestive of multicystic dysplastic kidney (MCDK), but postnatal imaging was atypical for this diagnosis given the location and singular cyst noted. The patient ultimately underwent surgical exploration and was diagnosed with an ectopic MCDK. Ectopic MCDK should be considered in the differential diagnosis of unilocular cystic pelvic lesions identified in the perinatal period.

摘要

我们报告了一例罕见的女性新生儿病例,该新生儿表现为单个中线盆腔囊肿。产前影像学检查提示多囊性发育不良肾(MCDK),但产后影像学检查因囊肿的位置和单个囊肿的发现而不符合该诊断。该患者最终接受了手术探查,被诊断为异位MCDK。在围产期发现的单房囊性盆腔病变的鉴别诊断中应考虑异位MCDK。