Gutiérrez-González Jorge Aurelio, González De La Torre Emilia, Armijo-Borjón Edgar Alan, Alarcón-Sandoval Abraham Alexander, Reyna-Sepulveda Francisco Javier, Montes-Tapia Fernando Felix, Muñoz-Maldonado Gerardo Enrique
General Surgery Department, Hospital Universitario "Dr. José Eleuterio González" UANL, Monterrey, Mexico.
Department of Pediatrics, Hospital Universitario "Dr. José Eleuterio González" UANL, Monterrey, Mexico.
J Surg Case Rep. 2023 Jul 21;2023(7):rjad407. doi: 10.1093/jscr/rjad407. eCollection 2023 Jul.
The annular pancreas (AP) is an uncommon congenital anomaly, characterised by a circumferential envelope in the second portion of the duodenum. In recent years, some genetic component has been found in the etiology. A newborn full-term male, weighing at 1910 g at birth, had a history of intrauterine growth restriction and diagnosis of tetralogy of Fallot, Down syndrome and congenital hypothyroidism. Duodenal membrane is suspected after persistent postprandial vomiting and abdominal distension; his abdomen was distended, hyperresonant and soft. The gastroduodenal series showed data compatible with a duodenal membrane so exploratory laparotomy was performed, finding the pancreas completely wrapping the second portion of the duodenum, so a diamond-shaped-duodenoduodenostomy anastomosis was performed. The AP should be considered, especially in male neonates with postprandial vomiting, abdominal distension, who show some other congenital anomaly, and in the abdominal X-ray, the sign of the double bubble is observed.
环状胰腺是一种罕见的先天性异常,其特征为十二指肠第二部被胰腺组织环形包绕。近年来,病因学研究发现其发病存在一定的遗传因素。一名足月男婴,出生体重1910克,有子宫内生长受限病史,诊断为法洛四联症、唐氏综合征及先天性甲状腺功能减退症。患儿出现餐后持续性呕吐及腹胀,怀疑存在十二指肠隔膜;腹部膨隆,呈鼓音,质地柔软。胃十二指肠造影显示结果符合十二指肠隔膜表现,遂行剖腹探查术,术中发现胰腺完全包绕十二指肠第二部,于是进行了菱形十二指肠十二指肠吻合术。对于餐后呕吐、腹胀且合并其他先天性异常的男性新生儿,尤其是腹部X线检查出现双泡征时,应考虑环状胰腺的可能。