Rodríguez Sánchez C, Jara P, Díaz C, del Pozo F, Díez-Pardo J, Vázquez C
An Esp Pediatr. 1986 Aug;25(2):115-20.
Five cases of choledochal cyst diagnosed from 1976 to 1983 are presented. Four patients began in the neonatal period as a cholestatic syndrome resembling biliary atresia and one patient began later on as a cholangitis. It is important for diagnosis the use of ultrasounds and radionuclide hepatobiliary. Clinical course depends on early diagnosis and treatment, because there is often an atresia of the common hepatic duct associated.
本文报告了1976年至1983年间诊断出的5例胆总管囊肿病例。4例患者在新生儿期开始表现为类似胆道闭锁的胆汁淤积综合征,1例患者后来以胆管炎起病。超声和放射性核素肝胆显像检查对诊断很重要。临床病程取决于早期诊断和治疗,因为常伴有肝总管闭锁。