Ramakrishnan Pavithra, Dahiya Garima, Lindstrom Meghan, Thenappan Thenappan
Department of Medicine University of Minnesota Minneapolis Minnesota USA.
Cardiovascular Division, Department of Medicine University of Minnesota Minneapolis Minnesota USA.
Pulm Circ. 2023 Aug 15;13(3):e12278. doi: 10.1002/pul2.12278. eCollection 2023 Jul.
Pulmonary tumor thrombotic microangiopathy (PTTM) is an under-recognized cause of pulmonary hypertension and fulminant right ventricle failure. It is associated with a high mortality due to delay in diagnosis. We present two cases of PTTM, both diagnosed postmortem, highlighting the importance of timely identification and initiation of treatment for this near-fatal condition.
肺肿瘤血栓性微血管病(PTTM)是一种未得到充分认识的导致肺动脉高压和暴发性右心室衰竭的病因。由于诊断延迟,其死亡率很高。我们报告两例PTTM病例,均为死后诊断,强调了及时识别并启动针对这种近乎致命疾病的治疗的重要性。