Fukushima T, Yoshinaga S, Matsuda T, Tomonaga M, Takahashi S, Oita J, Nagamatsu K
No Shinkei Geka. 1986 Jun;14(7):909-16.
Four cases of syringomyelia, each were considered to have different pathogenesis of syrinx and presented different clinical and radiological pictures, are reported. Case I was associated with Chiari I malformation and the syrinx communicated with the fourth ventricle through the central canal, case 2 was associated with Chiari II malformation and the syrinx was not communicated with the fourth ventricle, case 3 was thought to be traumatic and case 4 to be arachnoiditis due to unknown etiology. Metrizamide CT myelography was most valuable diagnostic technique to disclose the syringomyelic cavity and its extension. The cases except case 1 showed central opacification without via fourth ventricle, suggesting transneural migration CSF as shown by Aubin et al. Surgical treatment, therefore, was different in each case to obtain normal CSF dynamics. Case 1 was treated by suboccipital craniectomy, muscle plugging to the obex and syringo-subarachnoid shunt. In case 2 syringo-cisternal shunt was done in addition to suboccipital craniectomy. In case 3 syringocisternal shunt was done after laminectomy. In case 4 syringo-peritoneal shunt was performed. All but case 4 were obtained favorable result and case 4 was unfavorable except the disappearance of girdle sensation. For traumatic or inflammatory syringomyelia with tight adhesion between pia and arachnoid membrane in subarachnoid space, syringocisternal shunt was good way to obtain normal CSF dynamics and was expected to relieve the neurological deterioration.
本文报告了4例脊髓空洞症患者,每例患者的脊髓空洞发病机制各异,临床表现和影像学表现也各不相同。病例1合并Chiari I畸形,脊髓空洞通过中央管与第四脑室相通;病例2合并Chiari II畸形,脊髓空洞与第四脑室不相通;病例3被认为是创伤性的;病例4病因不明,考虑为蛛网膜炎。甲泛葡胺CT脊髓造影是显示脊髓空洞腔及其延伸范围最有价值的诊断技术。除病例1外,其他病例均显示中央充盈缺损,无第四脑室通路,提示经神经迁移的脑脊液,正如奥宾等人所描述的那样。因此,为了恢复正常的脑脊液动力学,每个病例的手术治疗方法都有所不同。病例1采用枕下颅骨切除术、肌肉填塞枕大孔和脊髓空洞 - 蛛网膜下腔分流术。病例2除枕下颅骨切除外,还进行了脊髓空洞 - 脑池分流术。病例3在椎板切除术后进行了脊髓空洞 - 脑池分流术。病例4进行了脊髓空洞 - 腹腔分流术。除病例4外,其他病例均取得了良好的效果,病例4除束带感消失外效果不佳。对于蛛网膜下腔软脑膜和蛛网膜之间紧密粘连的创伤性或炎性脊髓空洞症,脊髓空洞 - 脑池分流术是恢复正常脑脊液动力学的良好方法,有望缓解神经功能恶化。