Headache Group, The Wolfson Sensory, Pain and Rehabilitation Centre, NIHR King's Clinical Research Facility, & SLaM Biomedical Research Centre, Institute of Psychiatry, Psychology and Neuroscience, King's College London, London SE5 9PJ, UK.
Department of Neurology, University of California, Los Angeles, CA 90095, USA.
Int J Mol Sci. 2023 Aug 11;24(16):12697. doi: 10.3390/ijms241612697.
Migraine is a disabling neurological disorder burdening patients globally. Through the increasing development of preclinical and clinical experimental migraine models, advancing appreciation of the extended clinical phenotype, and functional neuroimaging studies, we can further our understanding of the neurobiological basis of this highly disabling condition. Despite increasing understanding of the molecular and chemical architecture of migraine mechanisms, many areas require further investigation. Research over the last three decades has suggested that migraine has a strong genetic basis, based on the positive family history in most patients, and this has steered exploration into possibly implicated genes. In recent times, human genome-wide association studies and rodent genetic migraine models have facilitated our understanding, but most migraine seems polygenic, with the monogenic migraine mutations being considerably rarer, so further large-scale studies are required to elucidate fully the genetic underpinnings of migraine and the translation of these to clinical practice. The monogenic migraine mutations cause severe aura phenotypes, amongst other symptoms, and offer valuable insights into the biology of aura and the relationship between migraine and other conditions, such as vascular disease and sleep disorders. This review will provide an outlook of what is known about some monogenic migraine mutations, including familial hemiplegic migraine, familial advanced sleep-phase syndrome, and cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy.
偏头痛是一种全球性致残性神经系统疾病,使患者深受其苦。通过不断发展的临床前和临床实验性偏头痛模型,对扩展的临床表型和功能神经影像学研究的深入了解,我们可以进一步认识这种高度致残疾病的神经生物学基础。尽管对偏头痛发病机制的分子和化学结构有了更多的了解,但仍有许多领域需要进一步研究。过去三十年来的研究表明,偏头痛具有很强的遗传基础,大多数患者都有阳性家族史,这促使人们探索可能涉及的基因。近年来,人类全基因组关联研究和啮齿动物遗传偏头痛模型促进了我们的理解,但大多数偏头痛似乎是多基因的,单基因偏头痛突变则相当罕见,因此需要进一步开展大规模研究,以充分阐明偏头痛的遗传基础,并将这些研究转化为临床实践。这些单基因偏头痛突变导致严重的先兆症状等其他症状,为先兆的生物学以及偏头痛与其他疾病(如血管疾病和睡眠障碍)之间的关系提供了宝贵的见解。本文综述了一些已知的单基因偏头痛突变,包括家族性偏瘫性偏头痛、家族性睡眠相位提前综合征和伴皮质下梗死和白质脑病的常染色体显性遗传性脑动脉病。