Panackel Charles, Fawaz Mohammed, Jacob Mathew, Raja Kaiser
Integrated Liver Care, Aster Medcity, Kochi, Kerala, India.
King's College Hospital London, Dubai Hills, Dubai, United Arab Emirates.
J Clin Exp Hepatol. 2023 Sep-Oct;13(5):895-911. doi: 10.1016/j.jceh.2023.04.003. Epub 2023 Apr 18.
Respiratory symptoms and hypoxemia can complicate chronic liver disease and portal hypertension. Various pulmonary disorders affecting the pleura, lung parenchyma, and pulmonary vasculature are seen in end-stage liver disease, complicating liver transplantation (LT). Approximately 8% of cirrhotic patients in an intensive care unit develop severe pulmonary problems. These disorders affect waiting list mortality and posttransplant outcomes. A thorough history, physical examination, and appropriate laboratory tests help diagnose and assess the severity to risk stratify pulmonary diseases before LT. Hepatopulmonary syndrome (HPS), portopulmonary hypertension (POPH), and hepatic hydrothorax (HH) are respiratory consequences specific to cirrhosis and portal hypertension. HPS is seen in 5-30% of cirrhosis cases and is characterized by impaired oxygenation due to intrapulmonary vascular dilatations and arteriovenous shunts. Severe HPS is an indication of LT. The majority of patients with HPS resolve their hypoxemia after LT. When pulmonary arterial hypertension occurs in patients with portal hypertension, it is called POPH. All other causes of pulmonary arterial hypertension should be ruled out before labeling as POPH. Since severe POPH (mean pulmonary artery pressure [mPAP] >50 mm Hg) is a relative contraindication for LT, it is crucial to screen for POPH before LT. Those with moderate POPH (mPAP >35 mm Hg), who improve with medical therapy, will benefit from LT. A transudative pleural effusion called hepatic hydrothorax (HH) is seen in 5-10% of people with cirrhosis. Refractory cases of HH benefit from LT. In recent years, increasing clinical expertise and advances in the medical field have resulted in better outcomes in patients with moderate to severe pulmonary disorders, who undergo LT.
呼吸症状和低氧血症会使慢性肝病和门静脉高压症复杂化。在终末期肝病中可见到各种影响胸膜、肺实质和肺血管系统的肺部疾病,这使肝移植(LT)变得复杂。重症监护病房中约8%的肝硬化患者会出现严重的肺部问题。这些疾病会影响等待名单上的死亡率和移植后的结果。全面的病史、体格检查和适当的实验室检查有助于在肝移植前诊断和评估肺部疾病的严重程度以进行风险分层。肝肺综合征(HPS)、门静脉高压性肺动脉高压(POPH)和肝性胸腔积液(HH)是肝硬化和门静脉高压特有的呼吸后果。5%至30%的肝硬化病例中可见HPS,其特征是由于肺内血管扩张和动静脉分流导致氧合受损。严重的HPS是肝移植的指征。大多数HPS患者在肝移植后低氧血症得到缓解。当门静脉高压患者出现肺动脉高压时,称为POPH。在诊断为POPH之前,应排除所有其他肺动脉高压的原因。由于严重的POPH(平均肺动脉压[mPAP]>50 mmHg)是肝移植的相对禁忌证,因此在肝移植前筛查POPH至关重要。那些中度POPH(mPAP>35 mmHg)且经药物治疗后病情改善的患者将从肝移植中获益。一种称为肝性胸腔积液(HH)的漏出性胸腔积液在5%至10%的肝硬化患者中可见。HH的难治性病例可从肝移植中获益。近年来,临床专业知识的增加和医学领域的进展使中度至重度肺部疾病患者接受肝移植后有了更好的结果。