Department of Cell Biology, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, 2-5-1 Shikata-cho, Kita-ku, Okayama 700-8558, Japan.
Department of Medical Neurobiology, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, 2-5-1 Shikata-cho, Kita-ku, Okayama 700-8558, Japan.
J Biochem. 2023 Nov 30;174(6):533-548. doi: 10.1093/jb/mvad068.
Sterile alpha and Toll/interleukin receptor motif-containing protein 1 (SARM1) is a NAD+ hydrolase that plays a key role in axonal degeneration and neuronal cell death. We reported that c-Jun N-terminal kinase (JNK) activates SARM1 through phosphorylation at Ser-548. The importance of SARM1 phosphorylation in the pathological process of Parkinson's disease (PD) has not been determined. We thus conducted the present study by using rotenone (an inducer of PD-like pathology) and neurons derived from induced pluripotent stem cells (iPSCs) from healthy donors and a patient with familial PD PARK2 (FPD2). The results showed that compared to the healthy neurons, FPD2 neurons were more vulnerable to rotenone-induced stress and had higher levels of SARM1 phosphorylation. Similar cellular events were obtained when we used PARK2-knockdown neurons derived from healthy donor iPSCs. These events in both types of PD-model neurons were suppressed in neurons treated with JNK inhibitors, Ca2+-signal inhibitors, or by a SARM1-knockdown procedure. The degenerative events were enhanced in neurons overexpressing wild-type SARM1 and conversely suppressed in neurons overexpressing the SARM1-S548A mutant. We also detected elevated SARM1 phosphorylation in the midbrain of PD-model mice. The results indicate that phosphorylated SARM1 plays an important role in the pathological process of rotenone-induced neurodegeneration.
无菌α 和 Toll/白细胞介素受体结构域蛋白 1(SARM1)是一种 NAD+ 水解酶,在轴突变性和神经元细胞死亡中起关键作用。我们报道 c-Jun N 端激酶(JNK)通过 Ser-548 磷酸化激活 SARM1。SARM1 磷酸化在帕金森病(PD)的病理过程中的重要性尚未确定。因此,我们使用鱼藤酮(一种诱导 PD 样病理的诱导剂)和来自健康供体和家族性 PD PARK2(FPD2)患者的诱导多能干细胞(iPSC)衍生的神经元进行了本研究。结果表明,与健康神经元相比,FPD2 神经元对鱼藤酮诱导的应激更敏感,并且 SARM1 磷酸化水平更高。当我们使用来自健康供体 iPSC 的 PARK2 敲低神经元时,获得了类似的细胞事件。在用 JNK 抑制剂、Ca2+信号抑制剂或 SARM1 敲低程序处理的神经元中,这两种类型的 PD 模型神经元中的退行性事件均受到抑制。在过表达野生型 SARM1 的神经元中,退行性事件增强,而在过表达 SARM1-S548A 突变体的神经元中则受到抑制。我们还在 PD 模型小鼠的中脑中检测到 SARM1 磷酸化水平升高。结果表明,磷酸化的 SARM1 在鱼藤酮诱导的神经退行性变的病理过程中起重要作用。