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缓慢而稳定:一例进展缓慢的神经内分泌肿瘤

Slow and Steady: A Slowly Progressing Neuroendocrine Tumor.

作者信息

Zheng Christie, Al Shabeeb Reem, Shah Dipam, Sardana Nitin

机构信息

University of Virginia School of Medicine, Charlottesville, VA.

Department of Internal Medicine, Inova Fairfax Medical Campus, Falls Church, VA.

出版信息

ACG Case Rep J. 2023 Sep 21;10(9):e01147. doi: 10.14309/crj.0000000000001147. eCollection 2023 Sep.

DOI:10.14309/crj.0000000000001147
PMID:37744875
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10513232/
Abstract

Neuroendocrine tumors (NETs) are rare malignant tumors that arise from neuroendocrine cells throughout the body, most commonly in the gastrointestinal and respiratory tracts. We report a case of well-differentiated grade 2 NET with a computed tomography scan showing multiple liver lesions consistent with the liver lesions seen 11 years before diagnosis. This case highlights the possibility of an indolent or prolonged clinical course of metastatic NET with an unknown primary vs primary hepatic NET.

摘要

神经内分泌肿瘤(NETs)是一种罕见的恶性肿瘤,起源于全身的神经内分泌细胞,最常见于胃肠道和呼吸道。我们报告一例2级高分化NET病例,计算机断层扫描显示多个肝脏病变,与诊断前11年所见的肝脏病变一致。该病例突出了转移性NET伴未知原发灶与原发性肝NET具有惰性或延长临床病程的可能性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/de3c/10513232/c57b428cc8a6/ac9-10-e01147-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/de3c/10513232/4218b459ab40/ac9-10-e01147-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/de3c/10513232/c57b428cc8a6/ac9-10-e01147-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/de3c/10513232/4218b459ab40/ac9-10-e01147-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/de3c/10513232/c57b428cc8a6/ac9-10-e01147-g002.jpg

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本文引用的文献

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BMC Cancer. 2018 Nov 16;18(1):1122. doi: 10.1186/s12885-018-5057-3.
2
Primary hepatic neuroendocrine tumor case with a preoperative course of 26 years: A case report and literature review.原发性肝神经内分泌肿瘤病例,术前病程 26 年:病例报告及文献复习。
World J Gastroenterol. 2018 Jun 28;24(24):2640-2646. doi: 10.3748/wjg.v24.i24.2640.
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Nothing But NET: A Review of Neuroendocrine Tumors and Carcinomas.唯有 NET:神经内分泌肿瘤和癌综述。
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Patient-Reported Burden of a Neuroendocrine Tumor (NET) Diagnosis: Results From the First Global Survey of Patients With NETs.患者报告的神经内分泌肿瘤(NET)诊断负担:NET患者首次全球调查结果
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JAMA Oncol. 2017 Oct 1;3(10):1335-1342. doi: 10.1001/jamaoncol.2017.0589.
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The epidemiology of metastases in neuroendocrine tumors.神经内分泌肿瘤转移的流行病学
Int J Cancer. 2016 Dec 15;139(12):2679-2686. doi: 10.1002/ijc.30400. Epub 2016 Sep 9.
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Exploring the rising incidence of neuroendocrine tumors: a population-based analysis of epidemiology, metastatic presentation, and outcomes.探讨神经内分泌肿瘤发病率的上升:基于人群的流行病学、转移表现和结局分析。
Cancer. 2015 Feb 15;121(4):589-97. doi: 10.1002/cncr.29099. Epub 2014 Oct 13.
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Neuroendocrine tumors of the gastrointestinal tract: Case reports and literature review.胃肠道神经内分泌肿瘤:病例报告与文献综述
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