Pongratz D
Z Rheumatol. 1986 Jul-Aug;45(4):133-8.
Inflammatory myopathies are as a rule rare diseases of skeletal muscle. In the majority of cases noninfective autoimmunological reactions are assumed. Only few diseases have an infectious origin. From a myopathological point of view, polymyositis must be selected from interstitial nodular myositis. The most important clinical diagnosis is polymyositis/dermatomyositis. Additional nodular myositis can be found in many other connective tissue diseases. Rare conditions of polymyositis are to be separated from idiopathic cases. The therapy of acute polymyositis or dermatomyositis consists in corticosteroids, if necessary in combination with immunosuppressive drugs.
炎症性肌病通常是骨骼肌的罕见疾病。在大多数情况下,推测为非感染性自身免疫反应。只有少数疾病起源于感染。从肌病理学角度来看,多肌炎必须与间质性结节性肌炎相区分。最重要的临床诊断是多肌炎/皮肌炎。在许多其他结缔组织疾病中也可发现额外的结节性肌炎。罕见的多肌炎病例应与特发性病例区分开来。急性多肌炎或皮肌炎的治疗包括使用皮质类固醇,必要时联合免疫抑制药物。