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以多模态成像为特征的青年快速进展性原发性硬皮病心肌病

Rapidly Progressive Primary Scleroderma Cardiomyopathy in a Young Adult Characterized by Multimodality Imaging.

作者信息

Maidman Samuel D, Birjiniuk Joav, Donnino Robert, Basu Atreyee, Belmont H Michael, Goldberg Randal I, Kadosh Bernard S

机构信息

Leon H. Charney Division of Cardiology, Department of Medicine, NYU Grossman School of Medicine, New York, New York.

Department of Surgery, NYU Grossman School of Medicine, New York, New York.

出版信息

CASE (Phila). 2023 May 22;7(9):349-353. doi: 10.1016/j.case.2023.03.006. eCollection 2023 Sep.

Abstract

• Scleroderma-related heart disease is usually secondary to lung disease or PH. • Scleroderma rarely causes systolic HF in young patients or those without CAD. • A multimodality strategy should be used to characterize scleroderma cardiomyopathy.

摘要

• 硬皮病相关的心脏病通常继发于肺部疾病或肺动脉高压。

• 硬皮病很少在年轻患者或无冠心病的患者中引起收缩性心力衰竭。

• 应采用多模态策略来描述硬皮病性心肌病。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2931/10542747/90773d25092e/gr1.jpg

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