Romano Giuseppe, Cirillo Mario, Bonavita Simona, Toro Giuseppe, Di Pietro Andrea, Lavorgna Luigi, Maida Elisabetta, Pagliuca Francesca, Urraro Fabrizio, Coppola Cinzia, Lus Giacomo, Signoriello Elisabetta
Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.
MRI Research Center SUN-FISM, University of Campania "Luigi Vanvitelli", Naples, Italy.
Radiol Case Rep. 2023 Oct 7;18(12):4431-4434. doi: 10.1016/j.radcr.2023.09.033. eCollection 2023 Dec.
We present the case of a 48-year-old-woman with apparently isolated central nervous system Erdheim-Chester disease characterized by brainstem involvement. Erdheim-Chester disease is extremely rare and multisystem impairment should always be sought in the suspicion of such pathology.
我们报告一例48岁女性,患有以脑干受累为特征的明显孤立性中枢神经系统厄德里希-切斯特病。厄德里希-切斯特病极为罕见,怀疑存在这种病理情况时应始终寻找多系统损害。