Ophthalmic Surg Lasers Imaging Retina. 2023 Oct;54(10):574-579. doi: 10.3928/23258160-20230920-01. Epub 2023 Oct 1.
Retinal detachments (RDs) are a complication of X-linked retinoschisis (XLRS) with a poor prognosis. This study aims to report outcomes of XLRS-RD repair in pediatric patients.
The study is a retrospective analysis of pediatric patients undergoing vitreoretinal surgery for XLRS-RDs from 2000 to 2022.
Nine patients (11 eyes) met inclusion criteria. All patients were boys, with a mean age of 8 years. Most RDs arose inferiorly (64%). Seven (64%) detachments were macula-involving. Seven (64%) detachments were repaired with combined scleral buckling and vitrectomy, two (18%) detachments were repaired with vitrectomy alone, one (9%) detachment underwent a primary scleral buckling procedure, and one (9%) asymptomatic detachment with a pigment demarcation line was observed. Silicone oil was used in eight of nine (89%) eyes undergoing vitrectomy. Final visual acuity was 20/200 or better in eight (73%) eyes. One eye that underwent surgical intervention remained unattached at follow-up.
Surgical repair in patients with XLRSRDs was associated with successful reattachment, although visual prognosis varied. .
视网膜脱离（RD）是 X 连锁性视网膜劈裂症（XLRS）的并发症，预后较差。本研究旨在报告儿童 XLRS-RD 修复的结果。
本研究为回顾性分析，纳入 2000 年至 2022 年间行玻璃体视网膜手术治疗的儿童 XLRS-RD 患者。
9 名患者（11 只眼）符合纳入标准。所有患者均为男性，平均年龄 8 岁。大多数 RD 位于下方（64%）。7 只眼（64%）累及黄斑。7 只眼（64%）行巩膜扣带联合玻璃体切除术修复，2 只眼（18%）行单纯玻璃体切除术修复，1 只眼（9%）行原发性巩膜扣带术修复，1 只眼（9%）观察到无症状伴色素分界线的 RD。行玻璃体切除术的 8 只眼中有 8 只（89%）眼使用硅油。8 只眼（73%）最终视力达到 20/200 或更好。1 只眼经手术干预后仍未复位。
XLRS-RD 患者的手术修复与成功复位相关，但视力预后存在差异。
